{"id":4670,"date":"2019-12-17T09:42:29","date_gmt":"2019-12-17T09:42:29","guid":{"rendered":"https:\/\/endoscopiaterapeutica.net\/pt\/uncategorized\/mucocele-de-apendice-qual-o-papel-da-colonoscopia\/"},"modified":"2021-09-17T21:03:40","modified_gmt":"2021-09-17T21:03:40","slug":"mucocele-de-apendice-qual-o-papel-da-colonoscopia","status":"publish","type":"post","link":"https:\/\/endoscopiaterapeutica.net\/pt\/assuntosgerais\/mucocele-de-apendice-qual-o-papel-da-colonoscopia\/","title":{"rendered":"Mucocele de Ap\u00eandice &#8211; Qual o papel da Colonoscopia?!"},"content":{"rendered":"<h5><\/h5>\n<h5><strong>CONCEITO E CLASSIFICA\u00c7\u00c3O<\/strong><\/h5>\n<p>O termo Mucocele do Ap\u00eandice refere-se \u00e0 obstru\u00e7\u00e3o e dilata\u00e7\u00e3o do l\u00famen apendicular devido ao ac\u00famulo de subst\u00e2ncia mucoide.<\/p>\n<p>Apesar de frequentemente utilizado, esse termo \u00e9 amb\u00edguo, sendo mais apropriado para descrever uma apar\u00eancia de imagem ao inv\u00e9s de uma entidade patol\u00f3gica, uma vez que a\u00a0natureza e o comportamento cl\u00ednico das les\u00f5es mucinosas apendiculares\u00a0englobam desde processos neopl\u00e1sicos a n\u00e3o neopl\u00e1sicos, sejam benignos ou malignos.<\/p>\n<p>Embora a literatura mais antiga sobre o tema falhe na distin\u00e7\u00e3o entre les\u00f5es benignas e neopl\u00e1sicas, a classifica\u00e7\u00e3o das les\u00f5es mucinosas apendiculares sofreu um refinamento significativo ao longo dos anos. Em 2012, o Grupo Internacional de Oncologia de Superf\u00edcie Peritoneal (PSOGI) desenvolveu uma classifica\u00e7\u00e3o de consenso que ajudou a resolver grande parte da confus\u00e3o em torno da terminologia diagn\u00f3stica:<\/p>\n<p>&nbsp;<\/p>\n<ul>\n<li><strong>Les\u00f5es mucinosas\u00a0N\u00c3O NEOPL\u00c1SICAS\u00a0do ap\u00eandice<\/strong>\n<ul>\n<li><strong>Mucoceles simples ou cistos de reten\u00e7\u00e3o<\/strong>&#8211; caracterizados por altera\u00e7\u00f5es epiteliais degenerativas devido \u00e0 obstru\u00e7\u00e3o (por exemplo, fecalito) e distens\u00e3o, sem qualquer evid\u00eancia de hiperplasia da mucosa ou neoplasia. Tamb\u00e9m s\u00e3o chamadas de mucoceles inflamat\u00f3rias ou obstrutivas<\/li>\n<\/ul>\n<\/li>\n<\/ul>\n<p>&nbsp;<\/p>\n<ul>\n<li><strong>Les\u00f5es mucinosas NEOPL\u00c1SICAS\u00a0do ap\u00eandice<\/strong>\n<ul>\n<li><strong>P\u00f3lipos serrilhados do ap\u00eandice (5-25%) <\/strong>\u2013 Podem se apresentar com ou sem displasia. Apesar de lembrarem as les\u00f5es serrilhadas do c\u00f3lon, possuem caracter\u00edsticas moleculares diferentes<\/li>\n<li><strong>Neoplasias mucinosas do ap\u00eandice (63 a 84%)<\/strong>&#8211; s\u00e3o tumores mucinosos displ\u00e1sicos que podem ser classificadas como de baixo grau (LAMN) ou de alto grau (HAMN)<\/li>\n<li><strong>Adenocarcinomas mucinosos do ap\u00eandice (11 a 20%)<\/strong>\u2013 diferentemente das neoplasias mucinosas, apresentam um car\u00e1ter francamente infiltrativo. Eles podem ser classificados como adenocarcinomas mucinosos moderadamente diferenciados ou pouco diferenciados (presen\u00e7a de c\u00e9lulas em anel de sinete)<\/li>\n<\/ul>\n<\/li>\n<\/ul>\n<p>&nbsp;<\/p>\n<h5><strong>MANIFESTA\u00c7\u00c3O CL\u00cdNICA<\/strong><\/h5>\n<p>A mucocele do ap\u00eandice \u00e9 um achado incomum, com incid\u00eancia relatada de 0,2% a 0,3% das amostras de apendicectomia.<\/p>\n<p>Os pacientes geralmente s\u00e3o assintom\u00e1ticos (50% dos casos) ou apresentam sintomas inespec\u00edficos.<\/p>\n<p>O sintoma mais frequente \u00e9 dor abdominal no quadrante inferior direito. Uma massa abdominal \u00e9 ocasionalmente palp\u00e1vel. Com menos frequ\u00eancia, os pacientes podem apresentar dor tipo c\u00f3lica intermitente associada \u00e0 intussuscep\u00e7\u00e3o da mucocele; obstru\u00e7\u00e3o intestinal por efeito de massa; sangramento gastrointestinal; sintomas genitourin\u00e1rios devido \u00e0 obstru\u00e7\u00e3o do ureter direito ou bexiga; \u00a0abdome agudo por ruptura da mucocele ou sepse.<\/p>\n<p>&nbsp;<\/p>\n<h5><strong>DIAGN\u00d3STICO ENDOSC\u00d3PICO<\/strong><\/h5>\n<p>Uma propor\u00e7\u00e3o significativa de todas as mucoceles \u00e9 descoberta incidentalmente em imagens abdominais (TC, RNM, USG) e colonoscopias para investiga\u00e7\u00e3o de dor abdominal ou rastreamento de c\u00e2ncer colorretal, ou ainda \u00a0durante cirurgias abdominais n\u00e3o relacionadas.<\/p>\n<p>A apar\u00eancia endosc\u00f3pica t\u00edpica da mucocele \u00e9 de uma les\u00e3o subepitelial revestida por mucosa \u00edntegra e brilhante, projetando-se sobre o l\u00famen apendicular, com o \u00f3stio localizado no centro do abaulamento (\u201csinal do vulc\u00e3o\u201d), eventualmente entrando e saindo do ceco conforme a respira\u00e7\u00e3o, bem como com drenagem de exsudato inflamat\u00f3rio hialino.<\/p>\n<p>Por se tratarem de les\u00f5es subepiteliais, onde a mucosa subjacente \u00e9 normal, as bi\u00f3psias endosc\u00f3picas n\u00e3o s\u00e3o diagn\u00f3sticas e consequentemente n\u00e3o devem ser realizadas.<\/p>\n<div id=\"attachment_10471\" style=\"width: 1290px\" class=\"wp-caption aligncenter\"><a href=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2021\/08\/600H0007.jpg\" data-rel=\"penci-gallery-image-content\" ><img fetchpriority=\"high\" decoding=\"async\" aria-describedby=\"caption-attachment-10471\" class=\"wp-image-10471 size-full\" src=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2021\/08\/600H0007.jpg\" alt=\"\" width=\"1280\" height=\"1024\" \/><\/a><p id=\"caption-attachment-10471\" class=\"wp-caption-text\">&#8220;Sinal do Vulc\u00e3o&#8221; (Imagem: arquivo pessoal)<\/p><\/div>\n<div id=\"attachment_10473\" style=\"width: 1290px\" class=\"wp-caption aligncenter\"><a href=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2021\/08\/600H0003.jpg\" data-rel=\"penci-gallery-image-content\" ><img decoding=\"async\" aria-describedby=\"caption-attachment-10473\" class=\"wp-image-10473 size-full\" src=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2021\/08\/600H0003.jpg\" alt=\"\" width=\"1280\" height=\"1024\" \/><\/a><p id=\"caption-attachment-10473\" class=\"wp-caption-text\">Drenagem de exsudato inflamat\u00f3rio hialino (Imagem: arquivo pessoal)<\/p><\/div>\n<div id=\"attachment_10472\" style=\"width: 1290px\" class=\"wp-caption aligncenter\"><a href=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2021\/08\/600H0004.jpg\" data-rel=\"penci-gallery-image-content\" ><img decoding=\"async\" aria-describedby=\"caption-attachment-10472\" class=\"wp-image-10472 size-full\" src=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2021\/08\/600H0004.jpg\" alt=\"\" width=\"1280\" height=\"1024\" \/><\/a><p id=\"caption-attachment-10472\" class=\"wp-caption-text\">Aus\u00eancia de anormalidades \u00e0 cromoscopia virtual com NBI (Imagem: arquivo pessoal)<\/p><\/div>\n<p>&nbsp;<\/p>\n<p>A <strong>Ecoendoscopia<\/strong> (miniprobes) tamb\u00e9m pode ser realizada para ajudar a excluir outras les\u00f5es subepieliais, como lipomas, tumores neuroend\u00f3crinos e linfangiomas. A ultrassonografia endosc\u00f3pica pode confirmar a natureza c\u00edstica da mucocele, que se apresenta anec\u00f3ica ou hipoec\u00f3ica. Al\u00e9m disso, a invas\u00e3o estromal, sugestiva de adenocarcinoma mucinoso, tamb\u00e9m pode ser observada.\u00a0Pelos desafios no diagn\u00f3stico citol\u00f3gico dessas les\u00f5es e em virtude do risco da dissemina\u00e7\u00e3o peritoneal, n\u00e3o se recomenda pun\u00e7\u00e3o das mesmas.<\/p>\n<p>Nos pacientes onde a mucocele foi detectada incidentalmente pela colonoscopia, com ou sem Ecoendoscopia, uma TC abdominal deve ser realizada para confirmar o diagn\u00f3stico e excluir outras etiologias. Por outro lado, quando detectada atrav\u00e9s de imagens abdominais (TC, RNM ou USG), a colonoscopia tamb\u00e9m pode ser usada para avaliar exist\u00eancia de outras les\u00f5es apendiculares, bem como para determinar se h\u00e1 envolvimento do ceco, o que seria compat\u00edvel com a invas\u00e3o local de um adenocarcinoma.<\/p>\n<p>&nbsp;<\/p>\n<h5><strong>TRATAMENTO<\/strong><\/h5>\n<p>Mucoceles do ap\u00eandice menores que 2 cm raramente s\u00e3o malignas, enquanto aquelas maiores que 6 cm s\u00e3o geralmente consideradas malignas e \u00a0com alto risco de ruptura (20%).<\/p>\n<p>Embora seja uma doen\u00e7a rara, a apar\u00eancia endosc\u00f3pica da mucocele de ap\u00eandice \u00e9 caracter\u00edstica e permite um diagn\u00f3stico pr\u00e9-operat\u00f3rio preciso. O reconhecimento da doen\u00e7a e a ressec\u00e7\u00e3o cir\u00fargica s\u00e3o obrigat\u00f3rios devido ao potencial de transforma\u00e7\u00e3o maligna, bem como para impedir a ruptura da mesma, o que promove o desenvolvimento do pseudomixoma peritoneal.<\/p>\n<p>&nbsp;<\/p>\n<h5><strong>REFER\u00caNCIAS BIBLIOGR\u00c1FICAS<\/strong><\/h5>\n<ol>\n<li>Karakaya K et al. Appendiceal mucocele: Case reports and review of current literature. World J Gastroenterol 2008 April 14; 14(14): 2280-2283<\/li>\n<li>Zanati S et al. Colonoscopic diagnosis of mucocele of the appendix. GASTROINTESTINAL ENDOSCOPY Volume 62, No. 3 : 2005<\/li>\n<li>Cordero-Ruiz P et al. Appendiceal mucocele in a young patient \u2013 does size matter? Endoscopy 2011; 43: E243<\/li>\n<li>Ponsky J. An endoscopic view of mucocele of the appendix. GASTROINTESTINAL ENDOSCOPY Volume 23, No. 1 : 1976<\/li>\n<li>Nakagawa T. Colonoscopic diagnosis of mucocele of the appendix. GASTROINTESTINAL ENDOSCOPY Volume 39, No. 5 : 1993<\/li>\n<\/ol>\n","protected":false},"excerpt":{"rendered":"<p>CONCEITO E CLASSIFICA\u00c7\u00c3O O termo Mucocele do Ap\u00eandice refere-se \u00e0 obstru\u00e7\u00e3o e dilata\u00e7\u00e3o do&hellip;<\/p>\n","protected":false},"author":2079,"featured_media":4667,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"_lmt_disableupdate":"","_lmt_disable":"","footnotes":""},"categories":[151],"tags":[],"ano":[145],"tipo":[156],"volume":[147],"class_list":["post-4670","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-assuntosgerais","ano-145","tipo-colonoscopia","volume-volume-ii"],"yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v27.2 (Yoast SEO v27.4) - https:\/\/yoast.com\/product\/yoast-seo-premium-wordpress\/ -->\n<title>Mucocele de Ap\u00eandice - Qual o papel da Colonoscopia?! &#8226; Endoscopia Terapeutica<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/endoscopiaterapeutica.net\/pt\/assuntosgerais\/mucocele-de-apendice-qual-o-papel-da-colonoscopia\/\" \/>\n<meta property=\"og:locale\" content=\"pt_BR\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Mucocele de Ap\u00eandice - Qual o papel da Colonoscopia?!\" \/>\n<meta property=\"og:description\" content=\"CONCEITO E CLASSIFICA\u00c7\u00c3O O termo Mucocele do Ap\u00eandice refere-se \u00e0 obstru\u00e7\u00e3o e dilata\u00e7\u00e3o do l\u00famen apendicular devido ao ac\u00famulo de subst\u00e2ncia mucoide.\" \/>\n<meta property=\"og:url\" content=\"https:\/\/endoscopiaterapeutica.net\/pt\/assuntosgerais\/mucocele-de-apendice-qual-o-papel-da-colonoscopia\/\" \/>\n<meta property=\"og:site_name\" content=\"Endoscopia Terapeutica\" \/>\n<meta property=\"article:publisher\" content=\"https:\/\/www.facebook.com\/endoscopiaterapeutica\" \/>\n<meta property=\"article:author\" content=\"@gersonbrasiljr\" \/>\n<meta property=\"article:published_time\" content=\"2019-12-17T09:42:29+00:00\" \/>\n<meta property=\"article:modified_time\" content=\"2021-09-17T21:03:40+00:00\" \/>\n<meta property=\"og:image\" content=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2021\/08\/600H0007.jpg?v=1628201066\" \/>\n\t<meta property=\"og:image:width\" content=\"1280\" \/>\n\t<meta property=\"og:image:height\" content=\"1024\" \/>\n\t<meta property=\"og:image:type\" content=\"image\/jpeg\" \/>\n<meta name=\"author\" content=\"Gerson Brasil\" \/>\n<meta name=\"twitter:card\" content=\"summary_large_image\" \/>\n<meta name=\"twitter:label1\" content=\"Escrito por\" \/>\n\t<meta name=\"twitter:data1\" content=\"Gerson Brasil\" \/>\n\t<meta name=\"twitter:label2\" content=\"Est. tempo de leitura\" \/>\n\t<meta name=\"twitter:data2\" content=\"5 minutos\" \/>\n<script type=\"application\/ld+json\" class=\"yoast-schema-graph\">{\"@context\":\"https:\\\/\\\/schema.org\",\"@graph\":[{\"@type\":\"Article\",\"@id\":\"https:\\\/\\\/endoscopiaterapeutica.net\\\/pt\\\/assuntosgerais\\\/mucocele-de-apendice-qual-o-papel-da-colonoscopia\\\/#article\",\"isPartOf\":{\"@id\":\"https:\\\/\\\/endoscopiaterapeutica.net\\\/pt\\\/assuntosgerais\\\/mucocele-de-apendice-qual-o-papel-da-colonoscopia\\\/\"},\"author\":{\"name\":\"Gerson Brasil\",\"@id\":\"https:\\\/\\\/endoscopiaterapeutica.net\\\/pt\\\/#\\\/schema\\\/person\\\/65017be2c520fd19681b48b19bc8e830\"},\"headline\":\"Mucocele de Ap\u00eandice &#8211; Qual o papel da Colonoscopia?!\",\"datePublished\":\"2019-12-17T09:42:29+00:00\",\"dateModified\":\"2021-09-17T21:03:40+00:00\",\"mainEntityOfPage\":{\"@id\":\"https:\\\/\\\/endoscopiaterapeutica.net\\\/pt\\\/assuntosgerais\\\/mucocele-de-apendice-qual-o-papel-da-colonoscopia\\\/\"},\"wordCount\":935,\"commentCount\":0,\"publisher\":{\"@id\":\"https:\\\/\\\/endoscopiaterapeutica.net\\\/pt\\\/#organization\"},\"image\":{\"@id\":\"https:\\\/\\\/endoscopiaterapeutica.net\\\/pt\\\/assuntosgerais\\\/mucocele-de-apendice-qual-o-papel-da-colonoscopia\\\/#primaryimage\"},\"thumbnailUrl\":\"https:\\\/\\\/endoscopiaterapeutica.net\\\/pt\\\/wp-content\\\/uploads\\\/2021\\\/08\\\/600H0007.jpg?v=1628201066\",\"articleSection\":[\"Assuntos Gerais\"],\"inLanguage\":\"pt-BR\",\"potentialAction\":[{\"@type\":\"CommentAction\",\"name\":\"Comment\",\"target\":[\"https:\\\/\\\/endoscopiaterapeutica.net\\\/pt\\\/assuntosgerais\\\/mucocele-de-apendice-qual-o-papel-da-colonoscopia\\\/#respond\"]}]},{\"@type\":\"WebPage\",\"@id\":\"https:\\\/\\\/endoscopiaterapeutica.net\\\/pt\\\/assuntosgerais\\\/mucocele-de-apendice-qual-o-papel-da-colonoscopia\\\/\",\"url\":\"https:\\\/\\\/endoscopiaterapeutica.net\\\/pt\\\/assuntosgerais\\\/mucocele-de-apendice-qual-o-papel-da-colonoscopia\\\/\",\"name\":\"Mucocele de Ap\u00eandice - Qual o papel da Colonoscopia?! 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