{"id":4439,"date":"2017-04-24T09:20:38","date_gmt":"2017-04-24T09:20:38","guid":{"rendered":"https:\/\/endoscopiaterapeutica.net\/pt\/uncategorized\/tumor-de-celulas-granulares\/"},"modified":"2022-06-17T15:04:02","modified_gmt":"2022-06-17T15:04:02","slug":"tumor-de-celulas-granulares","status":"publish","type":"post","link":"https:\/\/endoscopiaterapeutica.net\/pt\/assuntosgerais\/tumor-de-celulas-granulares\/","title":{"rendered":"Tumor de c\u00e9lulas granulares do es\u00f4fago"},"content":{"rendered":"<p>Descrito inicialmente em 1926 por Abrikosoff&nbsp; como \u201cMioblastoma de c\u00e9lulas granulares\u201d. Tumor originado do tecido neural, das c\u00e9lulas de Schwann que fazem parte do plexo neuronal da submucosa esof\u00e1gica. Apresenta-se com tumor solit\u00e1rio em 90%, mas pode haver les\u00f5es multifocais&nbsp;em 10% dos casos. Maior acometimento dos 40 aos 60 anos.<\/p>\n<p>Locais mais comuns:<\/p>\n<ul>\n<li>L\u00edngua (40%), pele (30%), mama (15%) e trato respirat\u00f3rio (10%)<\/li>\n<li>Acometimento do TGI em apenas 8% dos tumores de c\u00e9lulas granulares<\/li>\n<li>No TGI o es\u00f4fago \u00e9 s\u00edtio mais comum de localiza\u00e7\u00e3o(30-60%), &nbsp;mas mesmo assim muito raro, correspondendo apenas a 2% de todos os tumores de c\u00e9lulas granulares<\/li>\n<\/ul>\n<p>&nbsp;<\/p>\n<p>Localiza\u00e7\u00e3o no es\u00f4fago: cervical (5-15%), m\u00e9dio (18-20%), distal (65-75%)<\/p>\n<p>&nbsp;<\/p>\n<p><strong>Diagn\u00f3stico:<\/strong><\/p>\n<p>Assintom\u00e1ticos<\/p>\n<p>Sintom\u00e1ticos:&nbsp; disfagia,&nbsp;dor retroesternal,&nbsp;regurgita\u00e7\u00e3o<\/p>\n<p>&nbsp;<\/p>\n<p>EDA:&nbsp; les\u00e3o subepitelial, elevada, s\u00e9ssil, nodular ou em placa, branco-amarelada, superf\u00edcie lisa ou levemente irregular, de consist\u00eancia fibroel\u00e1stica<\/p>\n<p>https:\/\/endoscopiaterapeutica.net\/pt\/tumor-de-celulas-granulares\/<\/p>\n<p>Histologia: imunohistoqu\u00edmica positiva para S-100 e para enolase neuroespec\u00edfica<\/p>\n<p>Ecoendoscopia:&nbsp;&nbsp; avalia profundidade,&nbsp; tamanho e&nbsp; invas\u00e3o muscular pr\u00f3pria. Achados: &nbsp;geralmente localizado at\u00e9 3\u00aa camada (submucosa), les\u00e3o bem delimitada, hipoecog\u00eanica.<\/p>\n<p><a href=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2021\/08\/miniprobe.png\" data-rel=\"penci-gallery-image-content\" ><img fetchpriority=\"high\" decoding=\"async\" class=\"alignnone size-full wp-image-7410\" src=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2021\/08\/miniprobe.png\" alt=\"miniprobe\" width=\"846\" height=\"349\"><\/a><\/p>\n<p><a href=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2021\/08\/eus.png\" data-rel=\"penci-gallery-image-content\" ><img decoding=\"async\" class=\"alignnone size-full wp-image-7411\" src=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2021\/08\/eus.png\" alt=\"eus\" width=\"840\" height=\"345\"><\/a><\/p>\n<p>&nbsp;<\/p>\n<p><strong>Diagn\u00f3stico diferencial:<\/strong><\/p>\n<p>Leiomioma: positivo para SMA e desmina<\/p>\n<p>GIST: raros no es\u00f4fago, positivo para CD117 e CD34<\/p>\n<p>&nbsp;<\/p>\n<p><strong>Progn\u00f3stico<\/strong><\/p>\n<p>Les\u00f5es benignas<\/p>\n<p>Menos de 2% com degenera\u00e7\u00e3o para malignidade<\/p>\n<p>Sinais de mau progn\u00f3stico: recorr\u00eancia local, &nbsp;crescimento r\u00e1pido, &gt; 4 cm, padr\u00e3o histol\u00f3gico, met\u00e1stase<\/p>\n<p>&nbsp;<\/p>\n<p><strong>Classifica\u00e7\u00e3o de Fanburg-Smith de maligniza\u00e7\u00e3o:<\/strong><\/p>\n<ul>\n<li>aumento da rela\u00e7\u00e3o n\u00facleo \/ citoplasma<\/li>\n<li>pleomorfismo nuclear<\/li>\n<li>n\u00facleo vesicular com nucl\u00e9olo proeminente<\/li>\n<li>necrose tumoral<\/li>\n<li>\u00edndice mit\u00f3tico aumentado (&gt; 2 por campo de grande aumento)<\/li>\n<\/ul>\n<p>&nbsp;<\/p>\n<p>Maligno: se tiver 3 ou mais dos crit\u00e9rios<\/p>\n<p>At\u00edpico: se tiver 1 ou 2 crit\u00e9rios<\/p>\n<p>Benigno: sem nenhum dos crit\u00e9rios acima<\/p>\n<p>&nbsp;<\/p>\n<p><strong>Conduta:<\/strong><\/p>\n<p>Seguimento \u2013 EDA com bi\u00f3psia anual em tumores menores que 10mm e assintom\u00e1ticos<\/p>\n<p>Indica\u00e7\u00e3o de tratamento: pacientes sintom\u00e1ticos, les\u00e3o maior que 1 cm, crescimento r\u00e1pido, suspeita de malignidade<\/p>\n<p>Tratamento endosc\u00f3pico: tumores pequenos (&lt; 2cm), sem invas\u00e3o da muscular pr\u00f3pria<\/p>\n<p>&nbsp;<\/p>\n<blockquote class=\"wp-embedded-content\" data-secret=\"1VRYTPPFG2\"><p><a href=\"https:\/\/endoscopiaterapeutica.net\/pt\/video\/reseccao-de-tumor-de-celulas-granulares\/\">Resec\u00e7\u00e3o de tumor de c\u00e9lulas granulares<\/a><\/p><\/blockquote>\n<p><iframe class=\"wp-embedded-content\" sandbox=\"allow-scripts\" security=\"restricted\" style=\"position: absolute; visibility: hidden;\" title=\"&#8220;Resec\u00e7\u00e3o de tumor de c\u00e9lulas granulares&#8221; &#8212; Endoscopia Terapeutica\" src=\"https:\/\/endoscopiaterapeutica.net\/pt\/video\/reseccao-de-tumor-de-celulas-granulares\/embed\/#?secret=AQpPB2eMfZ#?secret=1VRYTPPFG2\" data-secret=\"1VRYTPPFG2\" width=\"600\" height=\"338\" frameborder=\"0\" marginwidth=\"0\" marginheight=\"0\" scrolling=\"no\"><\/iframe><\/p>\n<p>&nbsp;<\/p>\n","protected":false},"excerpt":{"rendered":"<p>Descrito inicialmente em 1926 por Abrikosoff&nbsp; como \u201cMioblastoma de c\u00e9lulas granulares\u201d. Tumor originado do&hellip;<\/p>\n","protected":false},"author":1772,"featured_media":5153,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"_lmt_disableupdate":"","_lmt_disable":"","footnotes":""},"categories":[151],"tags":[],"ano":[276],"tipo":[153],"volume":[263],"class_list":["post-4439","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-assuntosgerais","ano-276","tipo-endoscopia-digestiva-alta","volume-volume-i"],"yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v27.2 (Yoast SEO v27.4) - https:\/\/yoast.com\/product\/yoast-seo-premium-wordpress\/ -->\n<title>Tumor de c\u00e9lulas granulares do es\u00f4fago &#8226; Endoscopia Terapeutica<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/endoscopiaterapeutica.net\/pt\/assuntosgerais\/tumor-de-celulas-granulares\/\" \/>\n<meta property=\"og:locale\" content=\"pt_BR\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Tumor de c\u00e9lulas granulares do es\u00f4fago\" \/>\n<meta property=\"og:description\" content=\"Descrito inicialmente em 1926 por Abrikosoff&nbsp; como \u201cMioblastoma de c\u00e9lulas granulares\u201d. 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