{"id":4378,"date":"2016-09-05T10:00:13","date_gmt":"2016-09-05T10:00:13","guid":{"rendered":"https:\/\/endoscopiaterapeutica.net\/pt\/uncategorized\/tumor-neuroendocrino-retal\/"},"modified":"2022-06-10T12:47:32","modified_gmt":"2022-06-10T12:47:32","slug":"tumor-neuroendocrino-retal","status":"publish","type":"post","link":"https:\/\/endoscopiaterapeutica.net\/pt\/assuntosgerais\/tumor-neuroendocrino-retal\/","title":{"rendered":"Revis\u00e3o: investiga\u00e7\u00e3o e manejo dos tumores neuroend\u00f3crinos retais"},"content":{"rendered":"<h1 style=\"text-align: center;\"><\/h1>\n<p>Os tumores neuroend\u00f3crinos (TNE) retais correspondem a 34% dos tumores neuroend\u00f3crinos do TGI, ficando atr\u00e1s em incid\u00eancia apenas dos TNE\u00a0de delgado.\u00a0A \u00a0incid\u00eancia de tumores neuroend\u00f3crinos retais tem se elevado muito ao longo dos \u00faltimos 35 anos, provavelmente devido ao aumento do n\u00famero de sigmoidoscopias e colonoscopias de rastreamento.\u00a0A maioria dos TNEs retais s\u00e3o diagnosticados acidentalmente, quando apresentam sintomas, sendo os mais comuns : sangramento retal, dor abdominal e emagrecimento.<\/p>\n<p>&nbsp;<\/p>\n<h5><strong>Padr\u00e3o histol\u00f3gico<\/strong><\/h5>\n<p>Os tumores neuroend\u00f3crinos retais expressam marcadores como cromogranina e sinaptofisina, embora nem sempre sejam positivo.<\/p>\n<p>O potencial de malignidade esta relacionado ao grau histol\u00f3gico graduado atrav\u00e9s do \u00edndice de mitoses e pelo marcador de prolifera\u00e7\u00e3o celular Ki-67, sendo classificados:<\/p>\n<ul>\n<li>Grau 1 (G1): Ki-67\u00a0 &lt;\u00a0 2%\u00a0\u00a0 \/\u00a0\u00a0 \u00edndice mit\u00f3tico &lt; 2 por 10 campos de grande aumento<\/li>\n<li>Grau 2 (G2):\u00a0 Ki-67\u00a0 &gt; 2%\u00a0 e\u00a0 &lt;\u00a0 20%\u00a0\u00a0 \/\u00a0\u00a0\u00a0 \u00edndice mit\u00f3tico &gt;2 e &lt;20 por 10 campos de grande aumento<\/li>\n<li>Grau 3 (G3): Ki-67\u00a0 &gt; 20%\u00a0 \/\u00a0\u00a0 \u00edndice mit\u00f3tico &gt; 20 por 10 campos de grande aumento<\/li>\n<\/ul>\n<p>&nbsp;<\/p>\n<h5><strong>Progn\u00f3stico<\/strong><\/h5>\n<p>O progn\u00f3stico dos TNE retais depende de alguns fatores como : tamanho menor que 20mm, grau histol\u00f3gico 1 (G1), aus\u00eancia de acometimento da muscular pr\u00f3pria, linfovascular e perineural.<\/p>\n<p>O acomentimento linfonodal pode estar presente em 60% nos tumores maiores que 20mm, 30% em tumores entre 10-20mm e at\u00e9 10% em tumores menores que 10mm.<\/p>\n<p>Vide mais:<\/p>\n<blockquote class=\"wp-embedded-content\" data-secret=\"9we3HqL3jG\"><p><a href=\"https:\/\/endoscopiaterapeutica.net\/pt\/artigoscomentados\/endoscopically-identified-well-differentiated-rectal-carcinoid-tumors-impact-of-tumor-size-on-the-natural-history-and-outcomes\/\">Tumor neuroend\u00f3crino retal bem diferenciado: o impacto do tamanho do tumor sobre a hist\u00f3ria natural e resultados terap\u00eauticos<\/a><\/p><\/blockquote>\n<p><iframe class=\"wp-embedded-content\" sandbox=\"allow-scripts\" security=\"restricted\" style=\"position: absolute; visibility: hidden;\" title=\"&#8220;Tumor neuroend\u00f3crino retal bem diferenciado: o impacto do tamanho do tumor sobre a hist\u00f3ria natural e resultados terap\u00eauticos&#8221; &#8212; Endoscopia Terapeutica\" src=\"https:\/\/endoscopiaterapeutica.net\/pt\/artigoscomentados\/endoscopically-identified-well-differentiated-rectal-carcinoid-tumors-impact-of-tumor-size-on-the-natural-history-and-outcomes\/embed\/#?secret=DAxLMTtAnE#?secret=9we3HqL3jG\" data-secret=\"9we3HqL3jG\" width=\"600\" height=\"338\" frameborder=\"0\" marginwidth=\"0\" marginheight=\"0\" scrolling=\"no\"><\/iframe><\/p>\n<p>&nbsp;<\/p>\n<p>Caracter\u00edsticas at\u00edpicas na apresenta\u00e7\u00e3o endosc\u00f3pica das les\u00f5es como : eros\u00e3o, superf\u00edcie irregular, base pediculada e colora\u00e7\u00e3o enantem\u00e1tica, tamb\u00e9m podem ser preditores de invas\u00e3o linfonodal. Ver mais:<\/p>\n<blockquote class=\"wp-embedded-content\" data-secret=\"JDtUMnxo1X\"><p><a href=\"https:\/\/endoscopiaterapeutica.net\/pt\/artigoscomentados\/clinical-impact-of-atypical-endoscopic-features-in-rectal-neuroendocrine-tumors\/\">Caracter\u00edsticas endosc\u00f3picas dos tumores neuroend\u00f3crinos retais podem prever met\u00e1stases linfonodais?<\/a><\/p><\/blockquote>\n<p><iframe class=\"wp-embedded-content\" sandbox=\"allow-scripts\" security=\"restricted\" style=\"position: absolute; visibility: hidden;\" title=\"&#8220;Caracter\u00edsticas endosc\u00f3picas dos tumores neuroend\u00f3crinos retais podem prever met\u00e1stases linfonodais?&#8221; &#8212; Endoscopia Terapeutica\" src=\"https:\/\/endoscopiaterapeutica.net\/pt\/artigoscomentados\/clinical-impact-of-atypical-endoscopic-features-in-rectal-neuroendocrine-tumors\/embed\/#?secret=Yyua8CYDPz#?secret=JDtUMnxo1X\" data-secret=\"JDtUMnxo1X\" width=\"600\" height=\"338\" frameborder=\"0\" marginwidth=\"0\" marginheight=\"0\" scrolling=\"no\"><\/iframe><\/p>\n<p>&nbsp;<\/p>\n<p>&nbsp;<\/p>\n<h5><strong>Tratamento inicial<\/strong><\/h5>\n<p>O endoscopista ao suspeitar de TNE, em uma les\u00e3o maior que 5mm, principalmente se apresentar sinais at\u00edpicos, n\u00e3o deve realizar a ressec\u00e7\u00e3o de imediato. O ideal \u00e9 realizar uma bi\u00f3psia para diagn\u00f3stico e estadiamento com Ki67, e se poss\u00edvel, realizar\u00a0ecoendoscopia para avalia\u00e7\u00e3o do acometimento profundo e de invas\u00e3o linfonodal. Somente ap\u00f3s isto deve-se optar pelo tratamento endosc\u00f3pico com t\u00e9cnicas de ressec\u00e7\u00e3o profunda (<strong><a href=\"https:\/\/endoscopiaterapeutica.net\/pt\/assuntosgerais\/resseccoes-endoscopicas\/\" target=\"_blank\" rel=\"noopener noreferrer\">ver mais<\/a><\/strong>), cirurgia transanal ou encaminhamento direto para cirurgia com linfadenectomia radical.<\/p>\n<p>Pacientes com indica\u00e7\u00e3o cir\u00fargica devem ser estadiados com RNM da pelve para melhor avalia\u00e7\u00e3o do acometimento linfonodal perif\u00e9rico. Exames como tomografia e PET-Scan podem ser usados para avalia\u00e7\u00e3o de met\u00e1stases a dist\u00e2ncia.<\/p>\n<div id=\"attachment_6581\" style=\"width: 1062px\" class=\"wp-caption alignnone\"><a href=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2021\/08\/CONDUTA-NO-TNE-RETAL.png\" data-rel=\"penci-gallery-image-content\" ><img fetchpriority=\"high\" decoding=\"async\" aria-describedby=\"caption-attachment-6581\" class=\"wp-image-6581 size-full\" src=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2021\/08\/CONDUTA-NO-TNE-RETAL.png\" alt=\"CONDUTA NO TNE RETAL\" width=\"1052\" height=\"724\" \/><\/a><p id=\"caption-attachment-6581\" class=\"wp-caption-text\">Investiga\u00e7\u00e3o e manejo dos tumores neuroend\u00f3crinos retais<\/p><\/div>\n<p>&nbsp;<\/p>\n<h5><strong>Tratamento secund\u00e1rio a ressec\u00e7\u00e3o incompleta<\/strong><\/h5>\n<p>Se o tratamento endosc\u00f3pico foi realizado e o anatomopatol\u00f3gico revelou margens laterais ou profunda acometidas, deve-se realizar uma avalia\u00e7\u00e3o criteriosa para a decis\u00e3o terap\u00eautica definitiva. Pode-se solicitar ecoendoscopia ou RNM da pelve para a pesquisa de acometimento linfonodal.<\/p>\n<p>Se n\u00e3o houver acometimento linfonodal e o TNE for de baixo grau (G1) pode-se tentar : uma nova ressec\u00e7\u00e3o profunda por mucosectomia, uma ressec\u00e7\u00e3o cir\u00fargica transanal ou ESD. A chance de complica\u00e7\u00f5es nessa nova tentativa de ressec\u00e7\u00e3o \u00e9 maior, portanto, idealmente, deve ser realizada por profissionais experientes.<\/p>\n<p>Lembrar que mesmo tumores menores que 10mm e sem caracter\u00edsticas at\u00edpicas podem apresentar acometimento linfonodal j\u00e1 ao diagn\u00f3stico e por isto cada caso deve ser individualizado e a decis\u00e3o tomada por equipe multidisciplinar.<\/p>\n<p>&nbsp;<\/p>\n<h5><strong>Tratamento cir\u00fargico<\/strong><\/h5>\n<p>O tratamento cir\u00fargico com linfadenectomia e excis\u00e3o total do mesorreto est\u00e1 indicado em :<\/p>\n<ul>\n<li>tumores maiores que 20mm<\/li>\n<li>alto grau histol\u00f3gico (G3) independente do tamanho<\/li>\n<li>na suspeita de acometimento linfonodal ou a dist\u00e2ncia.<\/li>\n<\/ul>\n<p><strong>\u00a0<\/strong><\/p>\n<p>&nbsp;<\/p>\n<h5><strong>Acompanhamento p\u00f3s tratamento<\/strong><\/h5>\n<p>&nbsp;<\/p>\n<div id=\"attachment_6612\" style=\"width: 811px\" class=\"wp-caption alignnone\"><a href=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2021\/08\/ACOMPANHAMENTO-POS-TRATAMENTO.png\" data-rel=\"penci-gallery-image-content\" ><img decoding=\"async\" aria-describedby=\"caption-attachment-6612\" class=\"size-full wp-image-6612\" src=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2021\/08\/ACOMPANHAMENTO-POS-TRATAMENTO.png\" alt=\"Est\u00e1gio 1\/T1 = tumor n\u00e3o invade a muscular pr\u00f3pria. Est\u00e1gio 2\/T2 = tumor invade a muscular pr\u00f3pria. Est\u00e1gio 3\/T3 = tumor ultrapassa a muscular pr\u00f3pria. Est\u00e1gio 4\/T4 = tumor ultrapassa a muscular pr\u00f3pria e invade o perit\u00f4neo e outros \u00f3rg\u00e3os. ED = Endoscopia Digestiva (Colonoscopia \/ Sigmoidoscopia)\" width=\"801\" height=\"558\" \/><\/a><p id=\"caption-attachment-6612\" class=\"wp-caption-text\">Est\u00e1gio 1\/T1 = tumor n\u00e3o invade a muscular pr\u00f3pria. Est\u00e1gio 2\/T2 = tumor invade a muscular pr\u00f3pria. Est\u00e1gio 3\/T3 = tumor ultrapassa a muscular pr\u00f3pria. Est\u00e1gio 4\/T4 = tumor ultrapassa a muscular pr\u00f3pria e invade o perit\u00f4neo e outros \u00f3rg\u00e3os. ED = Endoscopia Digestiva (Colonoscopia \/ Sigmoidoscopia)<\/p><\/div>\n<p>&nbsp;<\/p>\n<p><strong>Acesse o artigo original na \u00edntegra:<\/strong>\u00a0<a href=\"http:\/\/onlinelibrary.wiley.com\/doi\/10.1111\/apt.13697\/full\" target=\"_blank\" rel=\"noopener noreferrer\">Review article: the investigation and management of rectal neuroendocrine tumours.\u00a0R. Basuroy*, A. Haji*, J. K. Ramage*,\u2020, A. Quaglia\u2021 &amp; R. Srirajaskanthan<\/a><\/p>\n<p><b>Confira tamb\u00e9m: <\/b><a href=\"https:\/\/endoscopiaterapeutica.net\/pt\/quiz\/esquistossomose\">Quiz! \u2013 Qual seria sua hip\u00f3tese para esse achado na mucosa retal?<\/a><\/p>\n","protected":false},"excerpt":{"rendered":"<p>Os tumores neuroend\u00f3crinos (TNE) retais correspondem a 34% dos tumores neuroend\u00f3crinos do TGI, ficando&hellip;<\/p>\n","protected":false},"author":1772,"featured_media":3473,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"_lmt_disableupdate":"","_lmt_disable":"","footnotes":""},"categories":[151],"tags":[],"ano":[281],"tipo":[156,154],"volume":[147],"class_list":["post-4378","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-assuntosgerais","ano-281","tipo-colonoscopia","tipo-ecoendoscopia","volume-volume-ii"],"yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v27.2 (Yoast SEO v27.4) - 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