{"id":3841,"date":"2016-03-23T10:00:56","date_gmt":"2016-03-23T10:00:56","guid":{"rendered":"https:\/\/endoscopiaterapeutica.net\/pt\/uncategorized\/doenca-linfoproliferativa-pos-transplante\/"},"modified":"2022-06-17T15:33:53","modified_gmt":"2022-06-17T15:33:53","slug":"doenca-linfoproliferativa-pos-transplante","status":"publish","type":"post","link":"https:\/\/endoscopiaterapeutica.net\/pt\/casosclinicos\/doenca-linfoproliferativa-pos-transplante\/","title":{"rendered":"Doen\u00e7a linfoproliferativa p\u00f3s-transplante"},"content":{"rendered":"<h2 style=\"text-align: justify;\"><span style=\"text-decoration: underline;\"><strong>CASO CL\u00cdNICO<\/strong><\/span><\/h2>\n<p style=\"text-align: justify;\">Feminina, 4 anos, h\u00e1 1 semana com diarr\u00e9ia aquosa volumosa, com n\u00e1useas e febre (37,9\u00b0C), evolui h\u00e1 3 dias com enterorragia. Tem antecedente de transplante renal (intervivos) h\u00e1 6 meses, e faz uso de medica\u00e7\u00f5es imussupressoras: prednisona, everolimus e tacrolimus.&nbsp;Ao exame apresenta-se descorada e com sinais de desidrata\u00e7\u00e3o. Abd\u00f4men globoso, fl\u00e1cido, RHA+.<\/p>\n<p style=\"text-align: justify;\">Solicitada colonoscopia que evidenciou m\u00faltiplas \u00falceras ativas, profundas, recobertas por fibrina, com bordas bem delimitadas e elevadas, medindo de 10 a 30 mm, distribu\u00eddas por todo o c\u00f3lon (ver imagens abaixo):<\/p>\n<p style=\"text-align: justify;\"><a href=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2016\/03\/01275534.jpg\" data-rel=\"penci-gallery-image-content\"  rel=\"attachment wp-att-5389\"><img fetchpriority=\"high\" decoding=\"async\" class=\"alignnone size-medium wp-image-5389\" src=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2021\/08\/01275534.jpg\" alt=\"01275534\" width=\"300\" height=\"225\"><\/a> <a href=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2016\/03\/01275532.jpg\" data-rel=\"penci-gallery-image-content\"  rel=\"attachment wp-att-5390\"><img decoding=\"async\" class=\"alignnone size-medium wp-image-5390\" src=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2021\/08\/01275532.jpg\" alt=\"01275532\" width=\"300\" height=\"225\"><\/a> <a href=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2016\/03\/01275531.jpg\" data-rel=\"penci-gallery-image-content\"  rel=\"attachment wp-att-5391\"><img decoding=\"async\" class=\"alignnone size-medium wp-image-5391\" src=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2021\/08\/01275531.jpg\" alt=\"01275531\" width=\"300\" height=\"225\"><\/a> <a href=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2016\/03\/01275525.jpg\" data-rel=\"penci-gallery-image-content\"  rel=\"attachment wp-att-5392\"><img loading=\"lazy\" decoding=\"async\" class=\"alignnone size-medium wp-image-5392\" src=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2021\/08\/01275525.jpg\" alt=\"01275525\" width=\"300\" height=\"225\"><\/a> <a href=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2016\/03\/01275523.jpg\" data-rel=\"penci-gallery-image-content\"  rel=\"attachment wp-att-5393\"><img loading=\"lazy\" decoding=\"async\" class=\"alignnone size-medium wp-image-5393\" src=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2021\/08\/01275523.jpg\" alt=\"01275523\" width=\"300\" height=\"225\"><\/a> <a href=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2016\/03\/01275522.jpg\" data-rel=\"penci-gallery-image-content\"  rel=\"attachment wp-att-5394\"><img loading=\"lazy\" decoding=\"async\" class=\"size-medium wp-image-5394 alignright\" src=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2021\/08\/01275522.jpg\" alt=\"01275522\" width=\"300\" height=\"225\"><\/a><\/p>\n<p style=\"text-align: justify;\">Resultado das bi\u00f3psias (estudo anatomopatol\u00f3gico + imuno-histoqu\u00edmica):<\/p>\n<p style=\"text-align: justify;\"><strong>\u00dalceras com&nbsp;infiltrado&nbsp;linfoide&nbsp;at\u00edpico associadas ao Epstein-Barr v\u00edrus, ver nota:<\/strong><\/p>\n<ul style=\"text-align: justify;\">\n<li>Presen\u00e7a de moderado&nbsp;infiltrado linfoide, com alguns linf\u00f3citos&nbsp;maiores de padr\u00e3o imunobl\u00e1stico de permeio.<\/li>\n<li>Identificada positividade para o ant\u00edgeno do v\u00edrus Epstein-Barr em algumas destas c\u00e9lulas linfoides pelo estudo imuno-histoqu\u00edmico.<\/li>\n<\/ul>\n<p style=\"text-align: justify;\"><strong>Conclus\u00e3o:&nbsp;Deve ser considerada como hip\u00f3tese diagn\u00f3stica uma doen\u00e7a linfoproliferativa p\u00f3s-transplante (DLPT), forma precoce do tipo polim\u00f3rfica.<\/strong><\/p>\n<h2 style=\"text-align: justify;\"><strong>PET-CT demonstrou:<\/strong><\/h2>\n<p style=\"text-align: justify;\">Aumento focal do metabolismo em linfonodomegalias retroperitoneais, cervicais, axilares e inguinal \u00e0 direita. Focos de capta\u00e7\u00e3o tamb\u00e9m s\u00e3o observados no ba\u00e7o e f\u00edgado. O conjunto dos aspectos pode estar associado a suspeita cl\u00ednica de doen\u00e7a linfoproliferativa p\u00f3s-transplante.<\/p>\n<p style=\"text-align: justify;\">Neste caso foi iniciado tratamento com Rituximab.<\/p>\n<h2 style=\"text-align: justify;\"><span style=\"text-decoration: underline;\"><strong>REVIS\u00c3O<\/strong><\/span><\/h2>\n<p style=\"text-align: justify;\">A doen\u00e7a&nbsp;linfoproliferativa p\u00f3s-transplante (DLPT) \u00e9 uma complica\u00e7\u00e3o da imunossupress\u00e3o ap\u00f3s o transplante de \u00f3rg\u00e3o. A incid\u00eancia da DLPT&nbsp;varia&nbsp;de 2% a 20%, por\u00e9m sabe-se que ela \u00e9 maior em crian\u00e7as. A maior freq\u00fc\u00eancia da DLPT na popula\u00e7\u00e3o pedi\u00e1trica&nbsp;ocorre pois grande parte destes n\u00e3o haviam sido expostos ao Epstein-Barr v\u00edrus (EBV) antes do transplante, sendo, portanto, a soroconvers\u00e3o p\u00f3s-transplante um fator de risco significativo para o desenvolvimento da doen\u00e7a.<br \/>\nAcredita-se que o EBV desempenhe um papel central na patog\u00eanese da DLPT, sendo reportado que cerca de 80%&nbsp;dos casos est\u00e3o associados a esse v\u00edrus.<\/p>\n<p style=\"text-align: justify;\"><span style=\"line-height: 1.5;\">As manifesta\u00e7\u00f5es cl\u00ednicas da DLPT ocorrem mais frequentemente no primeiro ano ap\u00f3s o transplante, e podem afetar virtualmente qualquer \u00f3rg\u00e3o do corpo, focal ou difusamente.&nbsp;O trato gastrointestinal \u00e9 acometido em at\u00e9 20% dos casos. Sendo que o&nbsp;intestino delgado distal \u00e9 o mais comumente afetado. <\/span><\/p>\n<p style=\"text-align: justify;\"><span style=\"line-height: 1.5;\">Endoscopicamente pode-se observar desde mucosa com leves altera\u00e7\u00f5es, como edema, enantema difuso ou focal, eros\u00f5es, e at\u00e9 forma\u00e7\u00e3o de \u00falceras (como no caso apresentado). Por se tratar de uma&nbsp;condi\u00e7\u00e3o que pode ser agressiva e fatal, a endoscopia precoce com bi\u00f3psias, mesmo em&nbsp;casos com sintomas\/achados leves e inespec\u00edficos, \u00e9 aconselh\u00e1vel.<\/span><\/p>\n<p style=\"text-align: justify;\">As modalidades de tratamento da DLPT&nbsp;s\u00e3o variadas, incluindo redu\u00e7\u00e3o da terapia de imunossupress\u00e3o,&nbsp;controle da replica\u00e7\u00e3o do EBV, terapia antineopl\u00e1sica convencional (radioterapia, quimioterapia e cirurgia) e imunoterapia (anticorpos anti-c\u00e9lulas-B: rituximab).<\/p>\n<h2 style=\"text-align: justify;\"><strong>Refer\u00eancias:<\/strong><\/h2>\n<ol style=\"text-align: justify;\">\n<li class=\"cit\">Badham K, Mirchandani A, Arumainayagam N, West DR.&nbsp;<span class=\"highlight\">Epstein-Barr<\/span> <span class=\"highlight\">virus<\/span> <span class=\"highlight\">associated<\/span> with a <span class=\"highlight\">post<\/span>&#8211;<span class=\"highlight\">transplant<\/span> <span class=\"highlight\">lymphoproliferative<\/span> <span class=\"highlight\">disorder<\/span> <span class=\"highlight\">presenting<\/span> as <span class=\"highlight\">isolated<\/span><span class=\"highlight\">gastrointestinal<\/span> <span class=\"highlight\">tract<\/span> <span class=\"highlight\">bleeding<\/span>.&nbsp;Endoscopy. 2007;39(Suppl 1):E64-5.<\/li>\n<li class=\"cit\">Fernandes PM, Azeka E, Odoni V, Junqueira JJ, Bento GP, Aiello V, Barbero-Marcial M.&nbsp;<span class=\"highlight\">Post-transplantation<\/span> <span class=\"highlight\">lymphoproliferative disorder<\/span> in <span class=\"highlight\">pediatric<\/span> <span class=\"highlight\">patient<\/span>.&nbsp;Arq Bras Cardiol. 2006;87(4):e108-11.<\/li>\n<li class=\"cit\">Bitencourt AGV, Pinto&nbsp;PNV, Almeida MFA, Cerqueira&nbsp;WS, Assis&nbsp;AM, Rodrigues&nbsp;AMST, Chojniak R. Incidence and imaging findings of lymphoma after liver transplantation in children.&nbsp;Radiol Bras. 2012;45(1):7\u201311.<\/li>\n<\/ol>\n","protected":false},"excerpt":{"rendered":"<p>CASO CL\u00cdNICO Feminina, 4 anos, h\u00e1 1 semana com diarr\u00e9ia aquosa volumosa, com n\u00e1useas&hellip;<\/p>\n","protected":false},"author":3495,"featured_media":3842,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"_lmt_disableupdate":"","_lmt_disable":"","footnotes":""},"categories":[150],"tags":[],"ano":[281],"tipo":[156],"volume":[263],"class_list":["post-3841","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-casosclinicos","ano-281","tipo-colonoscopia","volume-volume-i"],"yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v27.2 (Yoast SEO v27.4) - https:\/\/yoast.com\/product\/yoast-seo-premium-wordpress\/ -->\n<title>Doen\u00e7a linfoproliferativa p\u00f3s-transplante &#8226; Endoscopia Terapeutica<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/endoscopiaterapeutica.net\/pt\/casosclinicos\/doenca-linfoproliferativa-pos-transplante\/\" \/>\n<meta property=\"og:locale\" content=\"pt_BR\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Doen\u00e7a linfoproliferativa p\u00f3s-transplante\" \/>\n<meta property=\"og:description\" content=\"CASO CL\u00cdNICO Feminina, 4 anos, h\u00e1 1 semana com diarr\u00e9ia aquosa volumosa, com n\u00e1useas e febre (37,9\u00b0C), evolui h\u00e1 3 dias com enterorragia. 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