{"id":3828,"date":"2016-04-06T10:00:11","date_gmt":"2016-04-06T10:00:11","guid":{"rendered":"https:\/\/endoscopiaterapeutica.net\/pt\/uncategorized\/caso-clinico\/"},"modified":"2022-06-15T14:41:54","modified_gmt":"2022-06-15T14:41:54","slug":"caso-clinico","status":"publish","type":"post","link":"https:\/\/endoscopiaterapeutica.net\/pt\/casosclinicos\/caso-clinico\/","title":{"rendered":"Neoplasia Mucinosa Papilar Intraductal (IPMN)"},"content":{"rendered":"<p style=\"text-align: justify;\">Paciente masculino de 84 anos foi referenciado ao nosso servi\u00e7o com hist\u00f3ria de dor abdominal, perda de peso, prurido e icter\u00edcia h\u00e1 3 meses. Os exames laboratoriais demonstraram&nbsp;colestase. Realizada TC de abd\u00f4men que evidenciou les\u00e3o expansiva em topografia da cabe\u00e7a pancre\u00e1tica associada a dilata\u00e7\u00e3o do Wirsung e m\u00faltiplas les\u00f5es c\u00edsticas distribu\u00eddas pelo corpo (imagem abaixo).<\/p>\n<p>&nbsp;<\/p>\n<p><a href=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2016\/04\/Captura_de_Tela_2016-04-06_a_s_09_.jpg\" data-rel=\"penci-gallery-image-content\"  rel=\"attachment wp-att-5589\"><img fetchpriority=\"high\" decoding=\"async\" class=\"size-medium wp-image-5589 aligncenter\" src=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2021\/08\/Captura_de_Tela_2016-04-06_a_s_09_.jpg\" alt=\"Captura_de_Tela_2016-04-06_a_s_09_\" width=\"300\" height=\"245\"><\/a><\/p>\n<p>&nbsp;<\/p>\n<p style=\"text-align: justify;\">Ap\u00f3s a passagem do aparelho at\u00e9 a segunda por\u00e7\u00e3o duodenal, observou-se a papila maior em posi\u00e7\u00e3o habitual, por\u00e9m o ducto pancre\u00e1tico encontrava-se entreaberto, com sa\u00edda de secre\u00e7\u00e3o espessa, e separado do \u00f3stio do ducto biliar (Figuras 1 e 2).<\/p>\n<p>&nbsp;<\/p>\n<p><a href=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2016\/04\/Captura_de_Tela_2016-04-06_a_s_10_.jpg\" data-rel=\"penci-gallery-image-content\"  rel=\"attachment wp-att-5591\"><img decoding=\"async\" class=\"size-medium wp-image-5591 aligncenter\" src=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2021\/08\/Captura_de_Tela_2016-04-06_a_s_10_.jpg\" alt=\"Captura_de_Tela_2016-04-06_a_s_10_\" width=\"300\" height=\"230\"><\/a><\/p>\n<p><a href=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2016\/04\/Captura_de_Tela_2016-04-06_a_s_10_-1.jpg\" data-rel=\"penci-gallery-image-content\"  rel=\"attachment wp-att-5590\"><img decoding=\"async\" class=\"size-medium wp-image-5590 aligncenter\" src=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2021\/08\/Captura_de_Tela_2016-04-06_a_s_10_-1.jpg\" alt=\"Captura_de_Tela_2016-04-06_a_s_10_ (1)\" width=\"300\" height=\"233\"><\/a><\/p>\n<p>&nbsp;<\/p>\n<p style=\"text-align: justify;\">A colangiopancreatografia retr\u00f3grada endosc\u00f3pica (CPRE)&nbsp;evidenciou estenose segmentar curta do col\u00e9doco distal e do ducto de Wirsung com&nbsp;dilata\u00e7\u00e3o de ambos os ductos a montante (Figura 3). Realizamos papilotomia t\u00e1tica (Figura 4) seguida da passagem de endopr\u00f3tese biliar pl\u00e1stica &#8211; 10 Fr x 7 cms &#8211; (Figura 5). Paciente foi contra-referenciado ao servi\u00e7o de origem para complementa\u00e7\u00e3o terap\u00eautica.<\/p>\n<p>&nbsp;<\/p>\n<p><a href=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2016\/04\/Captura_de_Tela_2016-04-06_a_s_10_-3.jpg\" data-rel=\"penci-gallery-image-content\"  rel=\"attachment wp-att-5592\"><img loading=\"lazy\" decoding=\"async\" class=\"size-medium wp-image-5592 aligncenter\" src=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2021\/08\/Captura_de_Tela_2016-04-06_a_s_10_-3.jpg\" alt=\"Captura_de_Tela_2016-04-06_a_s_10_ (3)\" width=\"300\" height=\"233\"><\/a><\/p>\n<p><a href=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2016\/04\/Captura_de_Tela_2016-04-06_a_s_10_-4.jpg\" data-rel=\"penci-gallery-image-content\"  rel=\"attachment wp-att-5593\"><img loading=\"lazy\" decoding=\"async\" class=\"size-medium wp-image-5593 aligncenter\" src=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2021\/08\/Captura_de_Tela_2016-04-06_a_s_10_-4.jpg\" alt=\"Captura_de_Tela_2016-04-06_a_s_10_ (4)\" width=\"300\" height=\"231\"><\/a><\/p>\n<p><a href=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2016\/04\/Captura_de_Tela_2016-04-06_a_s_10_-5.jpg\" data-rel=\"penci-gallery-image-content\"  rel=\"attachment wp-att-5594\"><img loading=\"lazy\" decoding=\"async\" class=\"size-medium wp-image-5594 aligncenter\" src=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2021\/08\/Captura_de_Tela_2016-04-06_a_s_10_-5.jpg\" alt=\"Captura_de_Tela_2016-04-06_a_s_10_ (5)\" width=\"300\" height=\"231\"><\/a><\/p>\n<p>&nbsp;<\/p>\n<p>Imagens gentilmente cedidas pelo Dr. Marcos Lera &#8211; M\u00e9dico Assistente do HC-FMUSP e do Hospital Israelita Albert Einstein.<\/p>\n<p><strong>Discuss\u00e3o<\/strong><\/p>\n<p style=\"text-align: justify;\">A neoplasia mucinosa papilar intraductal (IPMN) \u00e9 um tumor c\u00edstico do p\u00e2ncreas. Os primeiros relatos de IPMN datam do in\u00edcio da d\u00e9cada de 80. Sua incid\u00eancia ainda \u00e9 desconhecida, por\u00e9m a preval\u00eancia dessas neoplasias em um estudo realizado com a popula\u00e7\u00e3o de Minessota nos Estados Unidos, mostrou 2.04 casos para cada 100.000 hab. A etiologia permanece obscura, mas a evid\u00eancia atual&nbsp;sugere o envolvimento de v\u00e1rias vias respons\u00e1veis pelo aparecimento da neoplasia, incluindo uma associa\u00e7\u00e3o com s\u00edndromes heredit\u00e1rias. Os IPMNs ocorre mais comumente nos homens, com idade m\u00e9dia ao diagn\u00f3stico entre 64 e 67 anos. No momento do diagn\u00f3stico podem ainda ser benignos, com ou sem displasia, ou francamente malignos se apresentando j\u00e1 como um carcinoma invasivo. Em geral, os pequenos IPMNs localizados nos ramos secund\u00e1rios s\u00e3o benignos, particularmente em doentes assintom\u00e1ticos. Nesses casos podem ser seguidos de forma&nbsp;conservadora. Em contraste, os tumores do ducto principal devem ser ressecados e cuidadosamente examinados \u00e0 procura de um componente invasivo. Na aus\u00eancia de invas\u00e3o, a sobrevida \u00e9 excelente (94-100%). Mesmo os doentes em que se faz o diagn\u00f3stico de carcinoma invasivo (IPMNs associados) , o progn\u00f3stico \u00e9 melhor do que aqueles que apresentam adenocarcinoma ductal, com uma sobrevida de 5 anos de 40% a 60% em algumas s\u00e9ries. No entanto, nenhuma vantagem de sobrevida p\u00f4de ser demonstrada em rela\u00e7\u00e3o aos tipos histol\u00f3gicos (tubular convencional versus mucinosos). Diversas variantes histomorfol\u00f3gicas s\u00e3o reconhecidas, embora o significado cl\u00ednico desses \u201csubtipos\u201d ainda n\u00e3o est\u00e1 bem definido.<\/p>\n<p>&nbsp;<\/p>\n<p><strong>Bibliografia<\/strong><\/p>\n<p>&nbsp;<\/p>\n<p>1. Modolell I, Guarner L, Malagelada JR. Vagaries of clinical presentation of pancreatic and biliary tract cancer. Ann Oncol 1999; 10 Suppl 4:82.<\/p>\n<p>2. Porta M, Fabregat X, Malats N, et al. Exocrine pancreatic cancer: symptoms at presentation and their relation to tumour site and stage. Clin Transl Oncol 2005; 7:189.<\/p>\n<p>3. Varghese JC, Farrell MA, Courtney G, et al. Role of MR cholangiopancreatography in patients with failed or inadequate ERCP. AJR Am J Roentgenol 1999; 173:1527.<\/p>\n<p>4. K. M. Reid-Lombardo, J. St Sauver, Z. Li, W. A. Ahrens, K. K. Unni, and F. G. Que, \u201cIncidence, prevalence, and management of intraductal papillary mucinous neoplasm in Olmsted County, Minnesota, 1984\u20132005: a Population Study,\u201d Pancreas, vol. 37, no. 2, pp. 139\u2013144, 2008.<\/p>\n","protected":false},"excerpt":{"rendered":"<p>Paciente masculino de 84 anos foi referenciado ao nosso servi\u00e7o com hist\u00f3ria de dor&hellip;<\/p>\n","protected":false},"author":4256,"featured_media":3823,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"_lmt_disableupdate":"","_lmt_disable":"","footnotes":""},"categories":[150],"tags":[],"ano":[281],"tipo":[155,154],"volume":[263],"class_list":["post-3828","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-casosclinicos","ano-281","tipo-cpre","tipo-ecoendoscopia","volume-volume-i"],"yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v27.2 (Yoast SEO v27.4) - https:\/\/yoast.com\/product\/yoast-seo-premium-wordpress\/ -->\n<title>Neoplasia Mucinosa Papilar Intraductal (IPMN) &#8226; Endoscopia Terapeutica<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/endoscopiaterapeutica.net\/pt\/casosclinicos\/caso-clinico\/\" \/>\n<meta property=\"og:locale\" content=\"pt_BR\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Neoplasia Mucinosa Papilar Intraductal (IPMN)\" \/>\n<meta property=\"og:description\" content=\"Paciente masculino de 84 anos foi referenciado ao nosso servi\u00e7o com hist\u00f3ria de dor abdominal, perda de peso, prurido e icter\u00edcia h\u00e1 3 meses. 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