{"id":11241,"date":"2022-04-01T07:00:18","date_gmt":"2022-04-01T07:00:18","guid":{"rendered":"https:\/\/endoscopiaterapeutica.net\/pt\/?p=11241"},"modified":"2022-07-12T17:07:33","modified_gmt":"2022-07-12T17:07:33","slug":"sindrome-da-polipose-juvenil","status":"publish","type":"post","link":"https:\/\/endoscopiaterapeutica.net\/pt\/assuntosgerais\/sindrome-da-polipose-juvenil\/","title":{"rendered":"S\u00edndrome da Polipose Juvenil"},"content":{"rendered":"<h2>Defini\u00e7\u00e3o:<\/h2>\n<p>A s\u00edndrome da Polipose Juvenil (SPJ) \u00e9 caracterizada por predisposi\u00e7\u00e3o a p\u00f3lipos hamartomatosos no trato gastrointestinal.<\/p>\n<h4><em>Primeiramente, vamos lembrar o que s\u00e3o p\u00f3lipos hamartomatosos:<\/em><\/h4>\n<ul>\n<li>\n<h4><em>Os p\u00f3lipos hamartomatosos s\u00e3o compostos por elementos celulares normais, mas com arquitetura distorcida.<\/em><\/h4>\n<\/li>\n<li>\n<h4><em>As s\u00edndromes de polipose hamartomatosa incluem S\u00edndrome da Polipose Juvenil, S\u00edndrome de Peutz-Jeghers e S\u00edndrome do Tumor Hamartomatoso PTEN.<\/em><\/h4>\n<\/li>\n<li>\n<h4><em>As s\u00edndromes de polipose hamartomatosas s\u00e3o incomuns, e juntas s\u00e3o respons\u00e1veis por menos que 1% dos casos de c\u00e2ncer colorretal nos EUA.<\/em><\/h4>\n<\/li>\n<\/ul>\n<p>A SPJ \u00c9 uma condi\u00e7\u00e3o <strong>autoss\u00f4mica dominante<\/strong>, associada a muta\u00e7\u00e3o do gene SMAD4 ou BMPR1A. 75% dos pacientes t\u00eam hist\u00f3ria familiar positiva, mas 25% s\u00e3o muta\u00e7\u00e3o <em>de novo<\/em>. \u00c9 uma condi\u00e7\u00e3o rara, com incid\u00eancia na popula\u00e7\u00e3o geral de 1:100.000 \u2013 1:160.000 (Figuras 1 a 4)<\/p>\n<div id=\"attachment_11238\" style=\"width: 310px\" class=\"wp-caption aligncenter\"><img fetchpriority=\"high\" decoding=\"async\" aria-describedby=\"caption-attachment-11238\" class=\"size-medium wp-image-11238\" src=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/03\/spj-18-300x225.jpg\" alt=\"\" width=\"300\" height=\"225\" srcset=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/03\/spj-18-300x225.jpg?v=1648748165 300w, https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/03\/spj-18-585x439.jpg?v=1648748165 585w, https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/03\/spj-18.jpg?v=1648748165 640w\" sizes=\"(max-width: 300px) 100vw, 300px\" \/><p id=\"caption-attachment-11238\" class=\"wp-caption-text\">Figura 1<\/p><\/div>\n<div id=\"attachment_11236\" style=\"width: 310px\" class=\"wp-caption aligncenter\"><img decoding=\"async\" aria-describedby=\"caption-attachment-11236\" class=\"size-medium wp-image-11236\" src=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/03\/spj-15-300x225.jpg\" alt=\"\" width=\"300\" height=\"225\" srcset=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/03\/spj-15-300x225.jpg?v=1648748159 300w, https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/03\/spj-15-585x439.jpg?v=1648748159 585w, https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/03\/spj-15.jpg?v=1648748159 640w\" sizes=\"(max-width: 300px) 100vw, 300px\" \/><p id=\"caption-attachment-11236\" class=\"wp-caption-text\">Figura 2<\/p><\/div>\n<div id=\"attachment_11235\" style=\"width: 310px\" class=\"wp-caption aligncenter\"><img decoding=\"async\" aria-describedby=\"caption-attachment-11235\" class=\"size-medium wp-image-11235\" src=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/03\/spj-14-300x225.jpg\" alt=\"\" width=\"300\" height=\"225\" srcset=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/03\/spj-14-300x225.jpg?v=1648748156 300w, https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/03\/spj-14-585x439.jpg?v=1648748156 585w, https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/03\/spj-14.jpg?v=1648748156 640w\" sizes=\"(max-width: 300px) 100vw, 300px\" \/><p id=\"caption-attachment-11235\" class=\"wp-caption-text\">Figura 3<\/p><\/div>\n<div id=\"attachment_11232\" style=\"width: 310px\" class=\"wp-caption aligncenter\"><img loading=\"lazy\" decoding=\"async\" aria-describedby=\"caption-attachment-11232\" class=\"size-medium wp-image-11232\" src=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/03\/spj-7-300x225.jpg\" alt=\"\" width=\"300\" height=\"225\" srcset=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/03\/spj-7-300x225.jpg?v=1648748146 300w, https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/03\/spj-7-585x439.jpg?v=1648748146 585w, https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/03\/spj-7.jpg?v=1648748146 640w\" sizes=\"(max-width: 300px) 100vw, 300px\" \/><p id=\"caption-attachment-11232\" class=\"wp-caption-text\">Figura 4<\/p><\/div>\n<p>.<\/p>\n<p><strong>\u00a0<\/strong><\/p>\n<h2><strong>Apresenta\u00e7\u00e3o cl\u00ednica<\/strong><\/h2>\n<p>O n\u00famero de p\u00f3lipos varia, podendo indiv\u00edduos da mesma fam\u00edlia ter 4 \u2013 5 p\u00f3lipos por todo o tempo de vida, enquanto outros podem apresentar centenas.<\/p>\n<p>Os p\u00f3lipos est\u00e3o presentes em sua maioria no c\u00f3lon (98%) sendo mais comum no c\u00f3lon direito (70%), mas tamb\u00e9m podem estar presentes no est\u00f4mago (14%), duodeno (7%), jejuno e \u00edleo (7%). O tamanho varia de p\u00f3lipos s\u00e9sseis pequenos at\u00e9 p\u00f3lipos pediculados maiores que 3 cm, geralmente t\u00eam a superf\u00edcie lisa, enantematosa, podendo haver um exsutado esbranqui\u00e7ado em sua superf\u00edcie (Figuras 5 a 7).<\/p>\n<div id=\"attachment_11231\" style=\"width: 310px\" class=\"wp-caption aligncenter\"><img loading=\"lazy\" decoding=\"async\" aria-describedby=\"caption-attachment-11231\" class=\"size-medium wp-image-11231\" src=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/03\/spj-5-300x225.jpg\" alt=\"\" width=\"300\" height=\"225\" srcset=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/03\/spj-5-300x225.jpg?v=1648748143 300w, https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/03\/spj-5-585x439.jpg?v=1648748143 585w, https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/03\/spj-5.jpg?v=1648748143 640w\" sizes=\"(max-width: 300px) 100vw, 300px\" \/><p id=\"caption-attachment-11231\" class=\"wp-caption-text\">Figura 5<\/p><\/div>\n<div id=\"attachment_11230\" style=\"width: 310px\" class=\"wp-caption aligncenter\"><img loading=\"lazy\" decoding=\"async\" aria-describedby=\"caption-attachment-11230\" class=\"size-medium wp-image-11230\" src=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/03\/spj-4-300x225.jpg\" alt=\"\" width=\"300\" height=\"225\" srcset=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/03\/spj-4-300x225.jpg?v=1648748139 300w, https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/03\/spj-4-585x439.jpg?v=1648748139 585w, https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/03\/spj-4.jpg?v=1648748139 640w\" sizes=\"(max-width: 300px) 100vw, 300px\" \/><p id=\"caption-attachment-11230\" class=\"wp-caption-text\">Figura 6<\/p><\/div>\n<div id=\"attachment_11229\" style=\"width: 310px\" class=\"wp-caption aligncenter\"><img loading=\"lazy\" decoding=\"async\" aria-describedby=\"caption-attachment-11229\" class=\"size-medium wp-image-11229\" src=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/03\/spj-1-300x225.jpg\" alt=\"\" width=\"300\" height=\"225\" srcset=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/03\/spj-1-300x225.jpg?v=1648748136 300w, https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/03\/spj-1-585x439.jpg?v=1648748136 585w, https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/03\/spj-1.jpg?v=1648748136 640w\" sizes=\"(max-width: 300px) 100vw, 300px\" \/><p id=\"caption-attachment-11229\" class=\"wp-caption-text\">Figura 7<\/p><\/div>\n<p>Os sintomas come\u00e7am geralmente nas primeiras duas d\u00e9cadas de vida, e os mais comuns s\u00e3o sangramento e anemia (90%), mas os pacientes tamb\u00e9m podem apresentar dor abdominal, diarreia, intussuscep\u00e7\u00e3o e obstru\u00e7\u00e3o intestinal.<\/p>\n<p>A SPJ tamb\u00e9m pode estar associado a condi\u00e7\u00f5es extracol\u00f4nicas, como telangiectasia hemorr\u00e1gica heredit\u00e1ria, macrocefalia, hidroc\u00e9falo, coarcta\u00e7\u00e3o de aorta e tetralogia de Fallot.<\/p>\n<p><strong>\u00a0<\/strong><\/p>\n<h2><strong>Histologia<\/strong><\/h2>\n<p>A histologia mostra gl\u00e2ndulas dilatadas e ecctasiadas, com espa\u00e7os c\u00edsticos preenchidos por mucina, l\u00e2mina pr\u00f3pria abundante e infiltrado inflamat\u00f3rio cr\u00f4nico. <em><strong>Diferentemente de Peutz-Jeghers, n\u00e3o h\u00e1 prolifera\u00e7\u00e3o da camada muscular lisa<\/strong>.<\/em> \u00a0Cerca de 50% dos p\u00f3lipos tem \u00e1reas de adenoma.<\/p>\n<div id=\"attachment_12332\" style=\"width: 310px\" class=\"wp-caption aligncenter\"><a href=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/04\/glandula-dilatada-e-ectasiada.jpg\" data-rel=\"penci-gallery-image-content\" ><img loading=\"lazy\" decoding=\"async\" aria-describedby=\"caption-attachment-12332\" class=\"wp-image-12332 size-medium\" src=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/04\/glandula-dilatada-e-ectasiada-300x225.jpg\" alt=\"nota-se glandula dilatada e ectasiada\" width=\"300\" height=\"225\" srcset=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/04\/glandula-dilatada-e-ectasiada-300x225.jpg?v=1656012809 300w, https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/04\/glandula-dilatada-e-ectasiada-1024x768.jpg?v=1656012809 1024w, https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/04\/glandula-dilatada-e-ectasiada-768x576.jpg?v=1656012809 768w, https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/04\/glandula-dilatada-e-ectasiada-1536x1152.jpg?v=1656012809 1536w, https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/04\/glandula-dilatada-e-ectasiada-1920x1440.jpg?v=1656012809 1920w, https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/04\/glandula-dilatada-e-ectasiada-1170x878.jpg?v=1656012809 1170w, https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/04\/glandula-dilatada-e-ectasiada-585x439.jpg?v=1656012809 585w, https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/04\/glandula-dilatada-e-ectasiada.jpg?v=1656012809 2016w\" sizes=\"(max-width: 300px) 100vw, 300px\" \/><\/a><p id=\"caption-attachment-12332\" class=\"wp-caption-text\">nota-se gl\u00e2ndula dilatada e ectasiada<\/p><\/div>\n<div id=\"attachment_12333\" style=\"width: 310px\" class=\"wp-caption aligncenter\"><a href=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/04\/Notam-se-glandulas-dilatadas-e-ectasiadas-algumas-preenchidas-com-mucina-alem-de-congestao-vascular.jpg\" data-rel=\"penci-gallery-image-content\" ><img loading=\"lazy\" decoding=\"async\" aria-describedby=\"caption-attachment-12333\" class=\"wp-image-12333 size-medium\" src=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/04\/Notam-se-glandulas-dilatadas-e-ectasiadas-algumas-preenchidas-com-mucina-alem-de-congestao-vascular-300x225.jpg\" alt=\"Notam se glandulas dilatadas e ectasiadas algumas preenchidas com mucina alem de congestao vascular\" width=\"300\" height=\"225\" srcset=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/04\/Notam-se-glandulas-dilatadas-e-ectasiadas-algumas-preenchidas-com-mucina-alem-de-congestao-vascular-300x225.jpg?v=1656012817 300w, https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/04\/Notam-se-glandulas-dilatadas-e-ectasiadas-algumas-preenchidas-com-mucina-alem-de-congestao-vascular-1024x768.jpg?v=1656012817 1024w, https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/04\/Notam-se-glandulas-dilatadas-e-ectasiadas-algumas-preenchidas-com-mucina-alem-de-congestao-vascular-768x576.jpg?v=1656012817 768w, https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/04\/Notam-se-glandulas-dilatadas-e-ectasiadas-algumas-preenchidas-com-mucina-alem-de-congestao-vascular-1536x1152.jpg?v=1656012817 1536w, https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/04\/Notam-se-glandulas-dilatadas-e-ectasiadas-algumas-preenchidas-com-mucina-alem-de-congestao-vascular-1920x1440.jpg?v=1656012817 1920w, https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/04\/Notam-se-glandulas-dilatadas-e-ectasiadas-algumas-preenchidas-com-mucina-alem-de-congestao-vascular-1170x878.jpg?v=1656012817 1170w, https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/04\/Notam-se-glandulas-dilatadas-e-ectasiadas-algumas-preenchidas-com-mucina-alem-de-congestao-vascular-585x439.jpg?v=1656012817 585w, https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/04\/Notam-se-glandulas-dilatadas-e-ectasiadas-algumas-preenchidas-com-mucina-alem-de-congestao-vascular.jpg?v=1656012817 2016w\" sizes=\"(max-width: 300px) 100vw, 300px\" \/><\/a><p id=\"caption-attachment-12333\" class=\"wp-caption-text\">Notam-se gl\u00e2ndulas dilatadas e ectasiadas, algumas preenchidas com mucina, al\u00e9m de congest\u00e3o vascular<\/p><\/div>\n<div id=\"attachment_12334\" style=\"width: 310px\" class=\"wp-caption aligncenter\"><a href=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/04\/notam-se-glandulas-dilatadas-e-preenchidas-por-mucina-setas-amarelas_glandulas-normais-seta-azul.jpg\" data-rel=\"penci-gallery-image-content\" ><img loading=\"lazy\" decoding=\"async\" aria-describedby=\"caption-attachment-12334\" class=\"wp-image-12334 size-medium\" src=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/04\/notam-se-glandulas-dilatadas-e-preenchidas-por-mucina-setas-amarelas_glandulas-normais-seta-azul-300x225.jpg\" alt=\"Notam-se gl\u00e2ndulas dilatadas e preenchidas por mucina setas amarelas_glandulas normais seta azul\" width=\"300\" height=\"225\" srcset=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/04\/notam-se-glandulas-dilatadas-e-preenchidas-por-mucina-setas-amarelas_glandulas-normais-seta-azul-300x225.jpg?v=1656012826 300w, https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/04\/notam-se-glandulas-dilatadas-e-preenchidas-por-mucina-setas-amarelas_glandulas-normais-seta-azul-1024x768.jpg?v=1656012826 1024w, https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/04\/notam-se-glandulas-dilatadas-e-preenchidas-por-mucina-setas-amarelas_glandulas-normais-seta-azul-768x576.jpg?v=1656012826 768w, https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/04\/notam-se-glandulas-dilatadas-e-preenchidas-por-mucina-setas-amarelas_glandulas-normais-seta-azul-1536x1152.jpg?v=1656012826 1536w, https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/04\/notam-se-glandulas-dilatadas-e-preenchidas-por-mucina-setas-amarelas_glandulas-normais-seta-azul-1920x1440.jpg?v=1656012826 1920w, https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/04\/notam-se-glandulas-dilatadas-e-preenchidas-por-mucina-setas-amarelas_glandulas-normais-seta-azul-1170x878.jpg?v=1656012826 1170w, https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/04\/notam-se-glandulas-dilatadas-e-preenchidas-por-mucina-setas-amarelas_glandulas-normais-seta-azul-585x439.jpg?v=1656012826 585w, https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/04\/notam-se-glandulas-dilatadas-e-preenchidas-por-mucina-setas-amarelas_glandulas-normais-seta-azul.jpg?v=1656012826 2016w\" sizes=\"(max-width: 300px) 100vw, 300px\" \/><\/a><p id=\"caption-attachment-12334\" class=\"wp-caption-text\">Notam-se gl\u00e2ndulas dilatadas e preenchidas por mucina (setas amarelas); gl\u00e2ndulas normais representadas pela seta azul<\/p><\/div>\n<h2><strong>Risco de C\u00e2ncer<\/strong><\/h2>\n<ul>\n<li>Estes pacientes t\u00eam risco aumentado de c\u00e2ncer g\u00e1strico, colorretal, duodenal e p\u00e2ncreas.<\/li>\n<li>O risco de c\u00e2ncer colorretal varia de 17-22% aos 35 anos, chegando a 68% aos 60 anos.<\/li>\n<li>A incid\u00eancia de c\u00e2ncer no trato gastrointestinal superior pode chegar a 30%.<\/li>\n<\/ul>\n<p><strong>\u00a0<\/strong><\/p>\n<h2><strong>Diagn\u00f3stico<\/strong><\/h2>\n<p>O diagn\u00f3stico da SPJ exige o preenchimento de 1 dos seguintes crit\u00e9rios:<\/p>\n<ul>\n<li>Cinco ou mais p\u00f3lipos juvenis do c\u00f3lon e reto,<\/li>\n<li>P\u00f3lipos juvenis em outros segmentos do trato gastrointestinal<\/li>\n<li>Qualquer n\u00famero de p\u00f3lipos juvenis se hist\u00f3ria familiar positiva.<\/li>\n<\/ul>\n<h4><em><strong>Importante: A presen\u00e7a de p\u00f3lipos juvenis espor\u00e1dicos no c\u00f3lon n\u00e3o \u00e9 t\u00e3o incomum, estando presente em at\u00e9 2% das crian\u00e7as abaixo de 10 anos, sem caracterizar SPJ ou representar risco aumentado de c\u00e2ncer.<\/strong><\/em><\/h4>\n<h4><em><strong>\u00a0<\/strong><\/em><\/h4>\n<h2><strong>Rastreamento e vigil\u00e2ncia<\/strong><\/h2>\n<p>Para o rastreamento \/ vigil\u00e2ncia, o guideline da ACG de 2015 recomenda para os pacientes em risco:<\/p>\n<ul>\n<li>Colonoscopia inicialmente aos 12 anos ou quando iniciarem os sintomas, devendo ressecar os p\u00f3lipos maiores que 5 mm e repetir anualmente at\u00e9 erradica\u00e7\u00e3o dos p\u00f3lipos, depois pode-se espa\u00e7ar para 3\/3 anos.<\/li>\n<li>Endoscopia inicialmente aos 12 anos, repetir a cada 1-3 anos, devendo ressecar todos os p\u00f3lipos maiores que 5 mm.<\/li>\n<li>Estudo do delgado: Se houver p\u00f3lipos no duodeno, anemia ou enteropatia perdedora de prote\u00ednas, recomenda-se c\u00e1psula endosc\u00f3pica, enteroscopia ou enterotomografia<\/li>\n<\/ul>\n<p><strong>\u00a0<\/strong><\/p>\n<h2><strong>Tratamento:<\/strong><\/h2>\n<p>Pacientes com n\u00famero limitado de p\u00f3lipos podem ser manejados com polipectomia e vigil\u00e2ncia endosc\u00f3pica (Figuras 8 a 10).<\/p>\n<div id=\"attachment_11233\" style=\"width: 310px\" class=\"wp-caption aligncenter\"><img loading=\"lazy\" decoding=\"async\" aria-describedby=\"caption-attachment-11233\" class=\"size-medium wp-image-11233\" src=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/03\/spj-9-300x225.jpg\" alt=\"\" width=\"300\" height=\"225\" srcset=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/03\/spj-9-300x225.jpg?v=1648748149 300w, https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/03\/spj-9-585x439.jpg?v=1648748149 585w, https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/03\/spj-9.jpg?v=1648748149 640w\" sizes=\"(max-width: 300px) 100vw, 300px\" \/><p id=\"caption-attachment-11233\" class=\"wp-caption-text\">Figura 8<\/p><\/div>\n<div id=\"attachment_11237\" style=\"width: 310px\" class=\"wp-caption aligncenter\"><img loading=\"lazy\" decoding=\"async\" aria-describedby=\"caption-attachment-11237\" class=\"size-medium wp-image-11237\" src=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/03\/spj-16-300x225.jpg\" alt=\"\" width=\"300\" height=\"225\" srcset=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/03\/spj-16-300x225.jpg?v=1648748162 300w, https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/03\/spj-16-585x439.jpg?v=1648748162 585w, https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/03\/spj-16.jpg?v=1648748162 640w\" sizes=\"(max-width: 300px) 100vw, 300px\" \/><p id=\"caption-attachment-11237\" class=\"wp-caption-text\">Figura 9<\/p><\/div>\n<div id=\"attachment_11239\" style=\"width: 310px\" class=\"wp-caption aligncenter\"><img loading=\"lazy\" decoding=\"async\" aria-describedby=\"caption-attachment-11239\" class=\"size-medium wp-image-11239\" src=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/03\/spj-19-300x225.jpg\" alt=\"\" width=\"300\" height=\"225\" srcset=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/03\/spj-19-300x225.jpg?v=1648748168 300w, https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/03\/spj-19-585x439.jpg?v=1648748168 585w, https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2022\/03\/spj-19.jpg?v=1648748168 640w\" sizes=\"(max-width: 300px) 100vw, 300px\" \/><p id=\"caption-attachment-11239\" class=\"wp-caption-text\">Figura 10<\/p><\/div>\n<p>Colectomia com anastomose ileorretal \u00e9 indicado em caso de c\u00e2ncer, displasia de alto grau ou se n\u00e3o for poss\u00edvel controlar a polipose adequadamente. O reto no entanto deve permanecer em vigil\u00e2ncia endosc\u00f3pica.<\/p>\n<p>Proctocolectomia pode ser necess\u00e1ria dependendo do n\u00famero de p\u00f3lipos no reto. Metade dos pacientes submetidos a colectomia, v\u00e3o precisar de proctectomia posteriormente.<\/p>\n<p>Gastrectomia total ou parcial pode ser necess\u00e1ria para pacientes com displasia avan\u00e7ada, c\u00e2ncer g\u00e1strico ou polipose que n\u00e3o pode ser adequadamente controlada por endoscopia.<\/p>\n<p>\u00a0<\/p>\n<h3><strong>Como citar esse artigo:<\/strong><\/h3>\n<p>Figueiredo LZ, Martins BC. S\u00edndrome da Polipose Juvenil. Endoscopia Terap\u00eautica. 2022; vol 1. Dispon\u00edvel em: endoscopiaterapeutica.net\/pt\/assuntosgerais\/sindrome-da-polipose-juvenil<\/p>\n<p>\u00a0<\/p>\n<h2><strong>Refer\u00eancias:<\/strong><\/h2>\n<p>Zbuk KM, Eng C. Hamartomatous polyposis syndromes. Nat Clin Pract Gastroenterol Hepatol. 2007 Sep;4(9):492-502. doi: 10.1038\/ncpgasthep0902. PMID: 17768394.<\/p>\n<p>Larsen Haidle J, MacFarland SP, Howe JR. Juvenile Polyposis Syndrome. 2003 May 13 [updated 2022 Feb 3]. In: Adam MP, Ardinger HH, Pagon RA, Wallace SE, Bean LJH, Gripp KW, Mirzaa GM, Amemiya A, editors. GeneReviews<sup>\u00ae<\/sup>\u00a0[Internet]. Seattle (WA): University of Washington, Seattle; 1993\u20132022. PMID: 20301642.<\/p>\n<p>Calva, Daniel, and James R Howe. \u201cHamartomatous polyposis syndromes.\u201d\u00a0<em>The Surgical clinics of North America<\/em>\u00a0vol. 88,4 (2008): 779-817, vii. doi:10.1016\/j.suc.2008.05.002<\/p>\n<p>Syngal S, Brand RE, Church JM, Giardiello FM, Hampel HL, Burt RW; American College of Gastroenterology. ACG clinical guideline: Genetic testing and management of hereditary gastrointestinal cancer syndromes. Am J Gastroenterol. 2015 Feb;110(2):223-62; quiz 263. doi: 10.1038\/ajg.2014.435. Epub 2015 Feb 3. PMID: 25645574; PMCID: PMC4695986.<\/p>\n\n\n\n\n\n\n\n","protected":false},"excerpt":{"rendered":"<p>Defini\u00e7\u00e3o: A s\u00edndrome da Polipose Juvenil (SPJ) \u00e9 caracterizada por predisposi\u00e7\u00e3o a p\u00f3lipos hamartomatosos&hellip;<\/p>\n","protected":false},"author":5544,"featured_media":11236,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"_lmt_disableupdate":"","_lmt_disable":"","footnotes":""},"categories":[151],"tags":[348,350,349,346,345,351],"ano":[309],"tipo":[156],"volume":[263],"class_list":["post-11241","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-assuntosgerais","tag-hamartomatoso","tag-juvenil","tag-polipo-juvenil","tag-polipos","tag-polipose","tag-polipose-juvenil","ano-309","tipo-colonoscopia","volume-volume-i"],"yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v27.2 (Yoast SEO v27.4) - https:\/\/yoast.com\/product\/yoast-seo-premium-wordpress\/ -->\n<title>S\u00edndrome da Polipose Juvenil &#8226; Endoscopia Terapeutica<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/endoscopiaterapeutica.net\/pt\/assuntosgerais\/sindrome-da-polipose-juvenil\/\" \/>\n<meta property=\"og:locale\" content=\"pt_BR\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"S\u00edndrome da Polipose Juvenil\" \/>\n<meta property=\"og:description\" content=\"Defini\u00e7\u00e3o: A s\u00edndrome da Polipose Juvenil (SPJ) \u00e9 caracterizada por predisposi\u00e7\u00e3o a p\u00f3lipos hamartomatosos no trato gastrointestinal. 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