{"id":10596,"date":"2021-11-23T06:00:26","date_gmt":"2021-11-23T06:00:26","guid":{"rendered":"https:\/\/endoscopiaterapeutica.net\/pt\/?p=10596"},"modified":"2022-05-25T22:10:19","modified_gmt":"2022-05-25T22:10:19","slug":"tumor-de-krukenberg","status":"publish","type":"post","link":"https:\/\/endoscopiaterapeutica.net\/pt\/assuntosgerais\/tumor-de-krukenberg\/","title":{"rendered":"Tumor de Krukenberg"},"content":{"rendered":"<p><span style=\"font-weight: 400;\">O tumor de Krukenberg (TK) caracteriza-se por uma les\u00e3o metast\u00e1tica ovariana proveniente do adenocarcinoma de c\u00e9lulas em anel de sinete rico em mucina. \u00c9 uma patologia incomum respons\u00e1vel por 1% a 2% das neoplasias ovarianas.<\/span><\/p>\n<p><span style=\"font-weight: 400;\">Foi descrito pela primeira vez em 1896 pelo ginecologista e patologista alem\u00e3o Friedrich Ernst Krukenberg (1871-1946), que suspeitava ser essa les\u00e3o um novo tipo de neoplasia prim\u00e1ria do ov\u00e1rio. A descoberta dessa como les\u00e3o metast\u00e1tica ovariana, de um tumor prim\u00e1rio epitelial, s\u00f3 foi realizada em 1902.<\/span><\/p>\n<p><span style=\"font-weight: 400;\">Os s\u00edtios prim\u00e1rios podem ser provenientes de diversos locais:<\/span><\/p>\n<ul>\n<li style=\"font-weight: 400;\" aria-level=\"1\"><span style=\"font-weight: 400;\">Est\u00f4mago: s\u00edtio mais frequente, correspondendo a cerca de 70% dos casos, principalmente no piloro, representado pelo adenocarcinoma de c\u00e9lulas em anel de sinete ou difuso;<\/span><\/li>\n<li style=\"font-weight: 400;\" aria-level=\"1\"><span style=\"font-weight: 400;\">C\u00f3lon e reto (adenocarcinoma);<\/span><\/li>\n<li style=\"font-weight: 400;\" aria-level=\"1\"><span style=\"font-weight: 400;\">Mama (carcinoma lobular invasivo);<\/span><\/li>\n<li style=\"font-weight: 400;\" aria-level=\"1\"><span style=\"font-weight: 400;\">Outros (ex: ves\u00edcula biliar, ap\u00eandice e intestino delgado).<\/span><\/li>\n<\/ul>\n<p><span style=\"font-weight: 400;\">Somando-se as incid\u00eancias de met\u00e1stases oriundas do est\u00f4mago e da topografia colorretal, elas totalizam aproximadamente 90% dos s\u00edtios prim\u00e1rios do TK. Portanto, em regi\u00f5es que apresentem alto \u00edndice de c\u00e2ncer g\u00e1strico, como em pa\u00edses asi\u00e1ticos, a incid\u00eancia do TK tamb\u00e9m \u00e9 elevada, podendo representar at\u00e9 20% das neoplasias do ov\u00e1rio.<\/span><\/p>\n<p><span style=\"font-weight: 400;\">O perfil epidemiol\u00f3gico \u00e9 representado por mulheres jovens, na fase pr\u00e9-menopausa, com idade m\u00e9dia de 40 a 45 anos, fato que difere o TK dos tumores prim\u00e1rios de ov\u00e1rio, que apresentam maior incid\u00eancia na sexta d\u00e9cada de vida.<\/span><\/p>\n<h2><b>Sintomas<\/b><\/h2>\n<p><span style=\"font-weight: 400;\">Os principais sintomas acarretados pelo TK surgem pelo efeito de massa ou devido ao desequil\u00edbrio da produ\u00e7\u00e3o hormonal.<\/span><\/p>\n<ul>\n<li style=\"font-weight: 400;\" aria-level=\"1\"><span style=\"font-weight: 400;\">Grandes massas ovarianas: dor ou distens\u00e3o abdominal, ascite, perda ponderal, dor p\u00e9lvica e dispareunia;<\/span><\/li>\n<li style=\"font-weight: 400;\" aria-level=\"1\"><span style=\"font-weight: 400;\">Produ\u00e7\u00e3o hormonal exacerbada: hirsutismo, irregularidade no ciclo menstrual ou sangramento naquelas p\u00f3s-menopausa.<\/span><\/li>\n<\/ul>\n<p><span style=\"font-weight: 400;\">Entretanto, o TK pode permanecer assintom\u00e1tico at\u00e9 em est\u00e1gios avan\u00e7ados ou gerar sintomas inespec\u00edficos.<\/span><\/p>\n<h2><b>Diagn\u00f3stico<\/b><\/h2>\n<p><span style=\"font-weight: 400;\">Em 1973, Serov e Scully definiram crit\u00e9rios para auxiliar no diagn\u00f3stico do TK que posteriormente foram adotados pela OMS. S\u00e3o estes:<\/span><\/p>\n<ul>\n<li style=\"font-weight: 400;\" aria-level=\"1\"><span style=\"font-weight: 400;\">Presen\u00e7a de neoplasia ovariana infiltrativa com c\u00e9lulas em anel de sinete preenchidas por mucina;<\/span><\/li>\n<li style=\"font-weight: 400;\" aria-level=\"1\"><span style=\"font-weight: 400;\">Presen\u00e7a do envolvimento estromal ou apenas a prolifera\u00e7\u00e3o sarcomatoide do estroma ovariano.<\/span><\/li>\n<\/ul>\n<p><span style=\"font-weight: 400;\">A imuno-histoqu\u00edmica tem um papel fundamental no diagn\u00f3stico, sendo o CK7 e CK20 os ant\u00edgenos mais utilizados. Se CK7 e CK20 positivos ou apenas o CK20 positivo, a les\u00e3o \u00e9 sugestiva de uma met\u00e1stase de TK, mas, se imunorreatividade positivo para CK7 e negativo para CK20, a les\u00e3o favorece um carcinoma de ov\u00e1rio prim\u00e1rio.<\/span><\/p>\n<p><span style=\"font-weight: 400;\">Outro par\u00e2metro \u00fatil \u00e9 o ant\u00edgeno carcinoembrion\u00e1rio (CEA). Se positivo juntamente \u00e0 imunorreatividade negativa para CA 125, a les\u00e3o favorece origem metast\u00e1tica.<\/span><\/p>\n<p><span style=\"font-weight: 400;\">Tabela 1. Rela\u00e7\u00e3o dos marcadores imuno-histoqu\u00edmicos dos tumores ovarianos.<\/span><\/p>\n<div class=\"pcrstb-wrap\"><table>\n<tbody>\n<tr>\n<td><b>TIPOS DE TUMORES<\/b><\/td>\n<td><b>CK7<\/b><\/td>\n<td><b>CK20<\/b><\/td>\n<td><b>CEA<\/b><\/td>\n<td><b>CA-125<\/b><\/td>\n<\/tr>\n<tr>\n<td><span style=\"font-weight: 400;\">TK g\u00e1strico e colorretal<\/span><\/td>\n<td><span style=\"font-weight: 400;\">&#8211;<\/span><\/td>\n<td><span style=\"font-weight: 400;\">+<\/span><\/td>\n<td><span style=\"font-weight: 400;\">+<\/span><\/td>\n<td><span style=\"font-weight: 400;\">&#8211;<\/span><\/td>\n<\/tr>\n<tr>\n<td><span style=\"font-weight: 400;\">Neoplasia ovariana 1\u00aa<\/span><\/td>\n<td><span style=\"font-weight: 400;\">+<\/span><\/td>\n<td><span style=\"font-weight: 400;\">&#8211;<\/span><\/td>\n<td><span style=\"font-weight: 400;\">&#8211;<\/span><\/td>\n<td><span style=\"font-weight: 400;\">+<\/span><\/td>\n<\/tr>\n<\/tbody>\n<\/table><\/div>\n<p><span style=\"font-weight: 400;\">Com o diagn\u00f3stico de TK, \u00e9 importante a investiga\u00e7\u00e3o pormenorizada em busca dos focos prim\u00e1rios, seja por meio de m\u00e9todos endosc\u00f3picos ou radiol\u00f3gicos.<\/span><\/p>\n<p><span style=\"font-weight: 400;\">Como o local da neoplasia prim\u00e1ria frequentemente \u00e9 o TGI, \u00e9 de extrema import\u00e2ncia a realiza\u00e7\u00e3o de endoscopia digestiva alta e colonoscopia. Devemos nos atentar aos pontos cegos do est\u00f4mago, como a regi\u00e3o da c\u00e1rdia, entre as pregas da grande curvatura do corpo, e at\u00e9 mesmo valorizar os sinais discretos, como o espessamento das pregas ou diminui\u00e7\u00e3o da expansibilidade g\u00e1strica.<\/span><\/p>\n<p><span style=\"font-weight: 400;\">Nos m\u00e9todos de imagem radiol\u00f3gicos (como a ultrassonografia, tomografia computadorizada ou resson\u00e2ncia magn\u00e9tica), o TK apresenta-se como massas ovarianas assim\u00e9tricas, complexas, s\u00f3lidas (em menor frequ\u00eancia c\u00edsticas), com propor\u00e7\u00f5es vari\u00e1veis e bilaterais.<\/span><\/p>\n<p><span style=\"font-weight: 400;\">O fato da bilateralidade em 80% dos casos, ocasionado por sua natureza metast\u00e1tica, \u00e9 de grande valia na realiza\u00e7\u00e3o do diagn\u00f3stico diferencial de outros tumores, como os carcinomas mucinosos ovarianos prim\u00e1rios, tumores carcinoides mucinosos e tumores de c\u00e9lulas de Sertoli e Sertoli-Leydig.<\/span><\/p>\n<h2><b>Vias de dissemina\u00e7\u00e3o<\/b><\/h2>\n<p><span style=\"font-weight: 400;\">A via de dissemina\u00e7\u00e3o mais aceita, se o s\u00edtio prim\u00e1rio for no est\u00f4mago, \u00e9 a via linf\u00e1tica retr\u00f3grada:<\/span><\/p>\n<ul>\n<li style=\"font-weight: 400;\" aria-level=\"1\"><span style=\"font-weight: 400;\">As c\u00e9lulas neopl\u00e1sicas metastizam-se para os linfonodos perig\u00e1stricos, formando \u00eambolos que bloqueiam o sistema linf\u00e1tico, e, pelo refluxo, alcan\u00e7am a linfa para\u00f3rtica e p\u00e9lvica;<\/span><\/li>\n<li style=\"font-weight: 400;\" aria-level=\"1\"><span style=\"font-weight: 400;\">Sendo os ov\u00e1rios t\u00e3o bem vascularizados, eles t\u00eam prefer\u00eancia pelo dep\u00f3sito de tais c\u00e9lulas.<\/span><\/li>\n<\/ul>\n<p><span style=\"font-weight: 400;\">Outras vias de dissemina\u00e7\u00e3o s\u00e3o a direta (transperitoneal) e a hematog\u00eanica.<\/span><\/p>\n<h2><b>Acompanhamento<\/b><\/h2>\n<p><span style=\"font-weight: 400;\">O marcador CA-125 pode ser um par\u00e2metro \u00fatil tanto para o rastreio de met\u00e1stases ovarianas (em pacientes com adenocarcinoma prim\u00e1rio do TGI) como para monitoriza\u00e7\u00e3o de doen\u00e7a ativa, marcador para an\u00e1lise da ressecabilidade cir\u00fargica e avalia\u00e7\u00e3o do progn\u00f3stico.<\/span><\/p>\n<h2><span style=\"font-weight: 400;\">\u00a0<\/span><b>Progn\u00f3stico<\/b><\/h2>\n<p><span style=\"font-weight: 400;\">Mesmo com os avan\u00e7os da medicina, o progn\u00f3stico do TK ainda permanece desfavor\u00e1vel, devido a seu car\u00e1ter metast\u00e1tico e a sua evolu\u00e7\u00e3o silenciosa (acaba sendo diagnosticado em est\u00e1gios avan\u00e7ados).<\/span><\/p>\n<ul>\n<li style=\"font-weight: 400;\" aria-level=\"1\"><span style=\"font-weight: 400;\">A taxa de sobrevida m\u00e9dia ap\u00f3s o diagn\u00f3stico \u00e9 menor que 2 anos;<\/span><\/li>\n<li style=\"font-weight: 400;\" aria-level=\"1\"><span style=\"font-weight: 400;\">Atualmente, nenhum tratamento curativo est\u00e1 dispon\u00edvel;<\/span><\/li>\n<li style=\"font-weight: 400;\" aria-level=\"1\"><span style=\"font-weight: 400;\">Tratamento cir\u00fargico \u00e9 indicado para pacientes jovens e h\u00edgidas com doen\u00e7a limitada;<\/span><\/li>\n<li style=\"font-weight: 400;\" aria-level=\"1\"><span style=\"font-weight: 400;\">Para pacientes sintom\u00e1ticas, o tratamento paliativo cir\u00fargico pode ser considerado ap\u00f3s discuss\u00e3o multidisciplinar.<\/span><\/li>\n<\/ul>\n<h2><b>Como citar este artigo<\/b><\/h2>\n<p><span style=\"font-weight: 400;\">Greg\u00f3rio JM. Tumor de Krukenberg. Endoscopia Terap\u00eautica; 2021. Dispon\u00edvel em: https:\/\/endoscopiaterapeutica.net\/pt\/uncategorized\/tumor-de-krukenberg\/<\/span><\/p>\n<h2><b>Refer\u00eancias<\/b><\/h2>\n<ol>\n<li style=\"font-weight: 400;\" aria-level=\"1\"><span style=\"font-weight: 400;\">Aziz M, Kasi A. Krukenberg Tumor. 2021 Jul 25. In: StatPearls [Internet]. Treasure Island (FL): StatPearls Publishing; 2021 Jan\u2013. PMID: 29489206.<\/span><\/li>\n<li style=\"font-weight: 400;\" aria-level=\"1\"><span style=\"font-weight: 400;\">Kube\u010dek O, Laco J, \u0160pa\u010dek J, Petera J, Kopeck\u00fd J, Kube\u010dkov\u00e1 A, Filip S. The pathogenesis, diagnosis, and management of metastatic tumors to the ovary: a comprehensive review. Clin Exp Metastasis. 2017 Jun;34(5):295-307. doi: 10.1007\/s10585-017-9856-8. Epub 2017 Jul 20. PMID: 28730323; PMCID: PMC5561159.<\/span><\/li>\n<li style=\"font-weight: 400;\" aria-level=\"1\"><span style=\"font-weight: 400;\">Al-Agha OM, Nicastri AD. An in-depth look at Krukenberg tumor: an overview. Arch Pathol Lab Med. 2006 Nov;130(11):1725-30. doi: 10.5858\/2006-130-1725-AILAKT. PMID: 17076540.<\/span><\/li>\n<li style=\"font-weight: 400;\" aria-level=\"1\"><span style=\"font-weight: 400;\">Lyngdoh BS, Dey B, Mishra J, Marbaniang E. Krukenberg tumor. Autops Case Rep. 2020 Apr 2;10(2):e2020163. doi: 10.4322\/acr.2020.163. PMID: 33344281; PMCID: PMC7703453.<\/span><\/li>\n<li style=\"font-weight: 400;\" aria-level=\"1\"><span style=\"font-weight: 400;\">Agnes A, Biondi A, Ricci R, Gallotta V, D&#8217;Ugo D, Persiani R. Krukenberg tumors: Seed, route and soil. Surg Oncol. 2017 Dec;26(4):438-445. doi: 10.1016\/j.suronc.2017.09.001. Epub 2017 Sep 12. PMID: 29113663.<\/span><\/li>\n<li style=\"font-weight: 400;\" aria-level=\"1\"><span style=\"font-weight: 400;\">Zulfiqar M, Koen J, Nougaret S, Bolan C, VanBuren W, McGettigan M, Menias C. Krukenberg Tumors: Update on Imaging and Clinical Features. AJR Am J Roentgenol. 2020 Oct;215(4):1020-1029. doi: 10.2214\/AJR.19.22184. Epub 2020 Jul 13. PMID: 32755184.<\/span><\/li>\n<\/ol>\n<p><span style=\"font-weight: 400;\">Acesse o <\/span><a href=\"https:\/\/endoscopiaterapeutica.net\/pt\/\"><span style=\"font-weight: 400;\">Endoscopia Terap\u00eautica<\/span><\/a><span style=\"font-weight: 400;\"> para tomar contato com mais <\/span><a href=\"https:\/\/endoscopiaterapeutica.net\/pt\/artigos-comentados\/\"><span style=\"font-weight: 400;\">artigos comentados<\/span><\/a><span style=\"font-weight: 400;\">, <\/span><a href=\"https:\/\/endoscopiaterapeutica.net\/pt\/assuntos-gerais\/\"><span style=\"font-weight: 400;\">assuntos gerais<\/span><\/a><span style=\"font-weight: 400;\">, <\/span><a href=\"https:\/\/endoscopiaterapeutica.net\/pt\/casos-clinicos\/\"><span style=\"font-weight: 400;\">casos cl\u00ednicos<\/span><\/a><span style=\"font-weight: 400;\">, <\/span><a href=\"https:\/\/endoscopiaterapeutica.net\/pt\/quiz\/\"><span style=\"font-weight: 400;\">quizzes<\/span><\/a><span style=\"font-weight: 400;\">, <\/span><a href=\"https:\/\/endoscopiaterapeutica.net\/pt\/classificacoes\/\"><span style=\"font-weight: 400;\">classifica\u00e7\u00f5es<\/span><\/a><span style=\"font-weight: 400;\"> e mais!<\/span><\/p>\n","protected":false},"excerpt":{"rendered":"<p>O tumor de Krukenberg (TK) caracteriza-se por uma les\u00e3o metast\u00e1tica ovariana proveniente do adenocarcinoma&hellip;<\/p>\n","protected":false},"author":5507,"featured_media":0,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"_lmt_disableupdate":"","_lmt_disable":"","footnotes":""},"categories":[151],"tags":[],"ano":[262],"tipo":[156,153],"volume":[147],"class_list":["post-10596","post","type-post","status-publish","format-standard","hentry","category-assuntosgerais","ano-262","tipo-colonoscopia","tipo-endoscopia-digestiva-alta","volume-volume-ii"],"yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v27.2 (Yoast SEO v27.4) - https:\/\/yoast.com\/product\/yoast-seo-premium-wordpress\/ -->\n<title>Tumor de Krukenberg &#8226; 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