{"id":5625,"date":"2019-10-12T04:01:56","date_gmt":"2019-10-12T04:01:56","guid":{"rendered":"https:\/\/endoscopiaterapeutica.net\/pt\/classificacao\/publish-40\/"},"modified":"2023-07-18T00:38:13","modified_gmt":"2023-07-18T00:38:13","slug":"todani-doenca-cistica-da-via-biliar","status":"publish","type":"classificacao","link":"https:\/\/endoscopiaterapeutica.net\/pt\/classificacao\/todani-doenca-cistica-da-via-biliar\/","title":{"rendered":"Classifica\u00e7\u00e3o de Todani &#8211; Doen\u00e7a c\u00edstica da via biliar"},"content":{"rendered":"\n<p>Os cistos biliares s\u00e3o dilata\u00e7\u00f5es c\u00edsticas que podem ocorrer isoladamente ou ser m\u00faltiplos ao longo da via&nbsp;biliar. Podem ocasionar&nbsp;complica\u00e7\u00f5es significativas, como estenoses ductais, forma\u00e7\u00e3o de c\u00e1lculos, colangite, cirrose biliar secund\u00e1ria e colangiocarcinoma.<\/p>\n\n\n\n<p>A apresenta\u00e7\u00e3o cl\u00e1ssica inclui a tr\u00edade de dor abdominal, icter\u00edcia e massa palp\u00e1vel. No entanto, a maioria dos pacientes ter\u00e1 apenas um ou dois elementos da tr\u00edade. Os cistos biliares tamb\u00e9m podem ser um achado incidental durante exames de imagem ou CPRE.<\/p>\n\n\n\n<p>Os cistos biliares s\u00e3o classificados de acordo com a classifica\u00e7\u00e3o de Todani. O tipo I \u00e9 o mais frequente (50-85%), seguido pelo tipo IVA.<\/p>\n\n\n\n<figure class=\"wp-block-image\"><a href=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2019\/10\/Todani-1.png\" data-rel=\"penci-gallery-image-content\" ><img fetchpriority=\"high\" decoding=\"async\" width=\"1010\" height=\"1112\" src=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2019\/10\/Todani-1.png\" alt=\"\" class=\"wp-image-16567\" srcset=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2019\/10\/Todani-1.png 1010w, https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2019\/10\/Todani-1-272x300.png 272w, https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2019\/10\/Todani-1-930x1024.png 930w, https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2019\/10\/Todani-1-768x846.png 768w, https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2019\/10\/Todani-1-585x644.png 585w\" sizes=\"(max-width: 1010px) 100vw, 1010px\" \/><\/a><\/figure>\n\n\n\n<figure class=\"wp-block-table is-style-regular\"><div class=\"pcrstb-wrap\"><table><tbody><tr><td>Tipo<\/td><td>Caracter\u00edstica<\/td><\/tr><tr><td><strong>I<\/strong>\n<p>&nbsp;<\/p>\n<p>A<\/p>\n<p>B<\/p>\n<p>C<\/p>\n<\/td><td>Cisto limitado ao trato biliar extra-hep\u00e1tico\n<p>&nbsp;<\/p>\n<p>Dilata\u00e7\u00e3o c\u00edstica sacular de toda via biliar extra-hep\u00e1tica<\/p>\n<p>Dilata\u00e7\u00e3o focal de um segmento da via biliar extra-hep\u00e1tica<\/p>\n<p>Dilata\u00e7\u00e3o fusiforme de toda via biliar extra-hep\u00e1tica<\/p>\n<\/td><\/tr><tr><td><strong>II<\/strong><\/td><td>Divert\u00edculo verdadeiro de ducto extra-hep\u00e1tico<\/td><\/tr><tr><td><strong>III<\/strong><\/td><td>Coledocele ou duplica\u00e7\u00e3o duodenal<\/td><\/tr><tr><td><strong>IV<\/strong>\n<p>&nbsp;<\/p>\n<p>A<\/p>\n<p>B<\/p>\n<\/td><td>M\u00faltiplos cistos\n<p>&nbsp;<\/p>\n<p>Cistos na via biliar intra e extra-hep\u00e1tica<\/p>\n<p>Cistos na via biliar extra-hep\u00e1tica<\/p>\n<\/td><\/tr><tr><td><strong>V<\/strong><\/td><td>Cistos intra-hep\u00e1ticos, sem acometimento extra-hep\u00e1tico (doen\u00e7a de Caroli)<\/td><\/tr><\/tbody><\/table><\/div><\/figure>\n\n\n\n<p>Os cistos biliares est\u00e3o associados a um risco aumentado de c\u00e2ncer, particularmente colangiocarcinoma. No geral, a incid\u00eancia de c\u00e2ncer est\u00e1 entre 10% e 30%. O c\u00e2ncer \u00e9 mais comum em pacientes idosos e naqueles com cistos tipo I e IV.<\/p>\n\n\n\n<p><strong>O tratamento vai depender do tipo de doen\u00e7a c\u00edstica:<\/strong><\/p>\n\n\n\n<ul class=\"wp-block-list\">\n<li>Tipo I ou IV &#8211; excis\u00e3o cir\u00fargica completa do cisto com hepatojejunostomia em Y de Roux;<\/li>\n\n\n\n<li>Tipo II &#8211; excis\u00e3o simples do cisto;<\/li>\n\n\n\n<li>Tipo III \u2013 esfincterotomia nos casos sintom\u00e1ticos ou assintom\u00e1ticos jovens (realizar bi\u00f3psias do epit\u00e9lio do cisto para excluir displasia;<\/li>\n\n\n\n<li>Tipo V \u2013 transplante de f\u00edgado.<\/li>\n<\/ul>\n\n\n\n<h2 class=\"wp-block-heading has-text-align-left\"><strong>Refer\u00eancias: <\/strong><\/h2>\n\n\n\n<ol class=\"wp-block-list\">\n<li>Todani T, Watanabe Y, Toki A, Morotomi Y. Classification of congenital biliary cystic disease: special reference to type Ic and IVA cysts with primary ductal stricture. J Hepatobiliary Pancreat Surg. 2003;10(5):340-4.<\/li>\n<\/ol>\n","protected":false},"excerpt":{"rendered":"<p>Os cistos biliares s\u00e3o dilata\u00e7\u00f5es c\u00edsticas que podem ocorrer isoladamente ou ser m\u00faltiplos ao&hellip;<\/p>\n","protected":false},"author":712,"featured_media":16567,"template":"","categoria_de_classificacao":[181],"class_list":["post-5625","classificacao","type-classificacao","status-publish","has-post-thumbnail","hentry","categoria_de_classificacao-vias-biliares"],"yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v27.2 (Yoast SEO v27.2) - https:\/\/yoast.com\/product\/yoast-seo-premium-wordpress\/ -->\n<title>Classifica\u00e7\u00e3o de Todani - Doen\u00e7a c\u00edstica da via biliar &#8226; Endoscopia Terapeutica<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/endoscopiaterapeutica.net\/pt\/classificacao\/todani-doenca-cistica-da-via-biliar\/\" \/>\n<meta property=\"og:locale\" content=\"pt_BR\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Classifica\u00e7\u00e3o de Todani - Doen\u00e7a c\u00edstica da via biliar\" \/>\n<meta property=\"og:description\" content=\"Os cistos biliares s\u00e3o dilata\u00e7\u00f5es c\u00edsticas que podem ocorrer isoladamente ou ser m\u00faltiplos ao&hellip;\" \/>\n<meta property=\"og:url\" content=\"https:\/\/endoscopiaterapeutica.net\/pt\/classificacao\/todani-doenca-cistica-da-via-biliar\/\" \/>\n<meta property=\"og:site_name\" content=\"Endoscopia Terapeutica\" \/>\n<meta property=\"article:publisher\" content=\"https:\/\/www.facebook.com\/endoscopiaterapeutica\" \/>\n<meta property=\"article:modified_time\" content=\"2023-07-18T00:38:13+00:00\" \/>\n<meta property=\"og:image\" content=\"https:\/\/endoscopiaterapeutica.net\/pt\/wp-content\/uploads\/2019\/10\/Todani-1.png\" \/>\n\t<meta property=\"og:image:width\" content=\"1010\" \/>\n\t<meta property=\"og:image:height\" content=\"1112\" \/>\n\t<meta property=\"og:image:type\" content=\"image\/png\" \/>\n<meta name=\"twitter:card\" content=\"summary_large_image\" \/>\n<meta name=\"twitter:label1\" content=\"Est. tempo de leitura\" \/>\n\t<meta name=\"twitter:data1\" content=\"2 minutos\" \/>\n<script type=\"application\/ld+json\" class=\"yoast-schema-graph\">{\"@context\":\"https:\/\/schema.org\",\"@graph\":[{\"@type\":\"WebPage\",\"@id\":\"https:\/\/endoscopiaterapeutica.net\/pt\/classificacao\/todani-doenca-cistica-da-via-biliar\/\",\"url\":\"https:\/\/endoscopiaterapeutica.net\/pt\/classificacao\/todani-doenca-cistica-da-via-biliar\/\",\"name\":\"Classifica\u00e7\u00e3o de Todani - Doen\u00e7a c\u00edstica da via biliar &#8226; 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